DEFICIENT PHOSPHORYLATION OF MANNOSE RESIDUES OF MANNAN IN FIBROBLASTS OF PATIENTS WITH MUCOLIPIDOSE-II AND MUCOLIPIDOSE-III

被引:5
作者
BENYOSEPH, Y
HAHN, LC
DEFRANCO, CL
NADLER, HL
机构
关键词
D O I
10.1042/bj1930651
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
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页码:651 / 654
页数:4
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