OPTIC ATROPHY IN ACUTE INTERMITTENT PORPHYRIA

被引:14
作者
DEFRANCISCO, M
SAVINO, PJ
SCHATZ, NJ
机构
[1] WILLS EYE HOSP,NEURO OPHTHALMOL UNIT,PHILADELPHIA,PA 19130
[2] THOMAS JEFFERSON UNIV,DEPT OPHTHALMOL,PHILADELPHIA,PA 19107
[3] UNIV PENN,DEPT OCEANOG,PHILADELPHIA,PA 19174
[4] UNIV PENN,DEPT NEUROL,PHILADELPHIA,PA 19174
关键词
D O I
10.1016/0002-9394(79)90147-8
中图分类号
R77 [眼科学];
学科分类号
100212 ;
摘要
A 24-year-old woman developed bilateral blindness after recovery from coma secondary to acute intermittent porphyria. Gradual return of vision in the right eye with a permanent unilateral visual field defect and optic atrophy followed. We believe the pathophysiologic mechanism was spasm of the vessels supplying the optic disk leading to ischemia and infarction of the optic nerve. © 1979.
引用
收藏
页码:221 / 224
页数:4
相关论文
共 17 条
[11]  
REYNON M, 1956, Ann Ocul (Paris), V189, P319
[12]   PORPHYRIAS AS INBORN ERRORS OF METABOLISM [J].
WALDENSTROM, J .
AMERICAN JOURNAL OF MEDICINE, 1957, 22 (05) :758-773
[13]   NEUROLOGICAL SYMPTOMS CAUSED BY SOCALLED ACUTE PORPHYRIA [J].
Waldenstrom, Jan .
ACTA PSYCHIATRICA ET NEUROLOGICA, 1939, 14 (1-2) :375-379
[14]  
WALSH FB, 1969, CLIN NEURO OPHTHALMO, P1133
[15]  
WATSON CJ, 1954, ADV INTERNAL MED, V6, P235
[16]   CONVULSIVE SEIZURES AS THE PRESENTING MANIFESTATION OF INTERMITTENT PORPHYRIA [J].
WIRTSCHAFTER, JD ;
TURNER, FW ;
DOW, RS .
NEUROLOGY, 1960, 10 (08) :787-792
[17]   OCULAR INVOLVEMENT IN ACUTE INTERMITTENT PORPHYRIA [J].
WOLTER, JR ;
CLARK, RL ;
KALLET, HA .
AMERICAN JOURNAL OF OPHTHALMOLOGY, 1972, 74 (04) :666-&