SELECTIVE, NONCOMPETITIVE ASSIMILATION OF BOVINE TESTICULAR BETA-GALACTOSIDASE AND BOVINE LIVER BETA-GLUCURONIDASE BY GENERALIZED GANGLIOSIDOSIS FIBROBLASTS

被引：8

作者：

HIEBER, V

DISTLER, J

MYEROWITZ, R

SCHMICKEL, RD

JOURDIAN, GW

机构：

[1] UNIV MICHIGAN,RACKHAM ARTHRITIS RES UNIT,ANN ARBOR,MI 48109

[2] UNIV MICHIGAN,DEPT PEDIAT,ANN ARBOR,MI 48109

[3] UNIV MICHIGAN,DEPT BIOL CHEM,ANN ARBOR,MI 48109

来源：

JOURNAL OF CLINICAL INVESTIGATION | 1980年 / 65卷 / 04期

关键词：

D O I：

10.1172/JCI109740

中图分类号：

R-3 [医学研究方法]; R3 [基础医学];

学科分类号：

1001 ;

摘要：

引用

页码：879 / 884

页数：6

共 33 条

[1]

BAHL OP, 1977, FED PROC, V36, P2119

[2]

BAYNES JW, 1976, J BIOL CHEM, V251, P6016

[3] IN-VITRO CORRECTION OF DEFICIENT HUMAN FIBROBLASTS BY BETA-GLUCURONIDASE FROM DIFFERENT HUMAN SOURCES [J].

BROT, FE ;

GLASER, JH ;

ROOZEN, KJ ;

SLY, WS .

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1974, 57 (01) :1-8

[4] SANDHOFF DISEASE - DEFECTIVE GLYCOSAMINOGLYCAN CATABOLISM IN CULTURED FIBROBLASTS AND ITS CORRECTION BY BETA-N-ACETYLHEXOSAMINIDASE [J].

CANTZ, M ;

KRESSE, H .

EUROPEAN JOURNAL OF BIOCHEMISTRY, 1974, 47 (03) :581-590

[5] IDENTIFICATION OF MANNOSE 6-PHOSPHATE IN GLYCOPROTEINS THAT INHIBIT THE ASSIMILATION OF BETA-GALACTOSIDASE BY FIBROBLASTS [J].

DISTLER, J ;

HIEBER, V ;

SAHAGIAN, G ;

SCHMICKEL, R ;

JOURDIAN, GW .

PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1979, 76 (09) :4235-4239

[6]

DISTLER J, 1977, FED P, V36, P2012

[7]

DISTLER J, 1979, CARBOHYDRATE PROTEIN, P163

[8]

DISTLER J, 1975, DISORDERS CONNECTI D, V5, P311

[9]

Distler J J, 1978, Methods Enzymol, V50, P514

[10] BETA-GLUCURONIDASE DEFICIENCY MUCOPOLYSACCHARIDOSIS - STUDIES IN CULTURED FIBROBLASTS [J].

HALL, CW ;

CANTZ, M ;

NEUFELD, EF .

ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1973, 155 (01) :32-38

← 1 2 3 4 →