DEFECTIVE GLYCINE CLEAVAGE SYSTEM IN NON-KETOTIC HYPERGLYCINEMIA - OCCURRENCE OF A LESS ACTIVE GLYCINE DECARBOXYLASE AND AN ABNORMAL AMINOMETHYL CARRIER PROTEIN

被引:53
作者
HIRAGA, K [1 ]
KOCHI, H [1 ]
HAYASAKA, K [1 ]
KIKUCHI, G [1 ]
NYHAN, WL [1 ]
机构
[1] UNIV CALIF SAN DIEGO,SCH MED,DEPT PEDIAT,LA JOLLA,CA 92093
关键词
D O I
10.1172/JCI110284
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
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页码:525 / 534
页数:10
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