DEMONSTRATION OF 26-HYDROXYLATION OF C27-STEROIDS IN HUMAN-SKIN FIBROBLASTS, AND A DEFICIENCY OF THIS ACTIVITY IN CEREBROTENDINOUS XANTHOMATOSIS

被引：77

作者：

SKREDE, S

BJORKHEM, I

KVITTINGEN, EA

BUCHMANN, MS

LIE, SO

EAST, C

GRUNDY, S

机构：

[1] UNIV OSLO,RIKSHOSP,INST PEDIAT RES,N-0027 OSLO 1,NORWAY

[2] KAROLINSKA INST,HUDDINGE UNIV HOSP,DEPT CLIN CHEM,S-10401 STOCKHOLM 60,SWEDEN

[3] KAROLINSKA INST,HUDDINGE UNIV HOSP,RES CTR,S-10401 STOCKHOLM 60,SWEDEN

[4] CTR HUMAN NUTR,DALLAS,TX

[5] DEPT INTERNAL MED,DALLAS,TX

来源：

JOURNAL OF CLINICAL INVESTIGATION | 1986年 / 78卷 / 03期

关键词：

D O I：

10.1172/JCI112633

中图分类号：

R-3 [医学研究方法]; R3 [基础医学];

学科分类号：

1001 ;

摘要：

引用

页码：729 / 735

页数：7

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[4] OMEGA-HYDROXYLATION OF STEROID SIDE-CHAIN IN BIOSYNTHESIS OF BILE-ACIDS [J].

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