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KINETIC AND IMMUNOCHEMICAL CHARACTERIZATION OF LOW-ACTIVITY SERUM ALPHA-L-FUCOSIDASE FROM A PHENOTYPICALLY NORMAL INDIVIDUAL
被引:12
作者
:
ALHADEFF, JA
论文数:
0
引用数:
0
h-index:
0
ALHADEFF, JA
ANDREWSSMITH, GL
论文数:
0
引用数:
0
h-index:
0
ANDREWSSMITH, GL
机构
:
来源
:
BIOCHEMICAL MEDICINE
|
1978年
/ 20卷
/ 03期
关键词
:
D O I
:
10.1016/0006-2944(78)90083-2
中图分类号
:
Q5 [生物化学];
Q7 [分子生物学];
学科分类号
:
071010 ;
081704 ;
摘要
:
引用
收藏
页码:357 / 363
页数:7
相关论文
共 16 条
[1]
ISOENZYME PATTERNS OF HUMAN LIVER ALPHA-L-FUCOSIDASE DURING DEVELOPMENT
ALHADEFF, JA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
ALHADEFF, JA
TENNANT, L
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
TENNANT, L
OBRIEN, JS
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
OBRIEN, JS
[J].
DEVELOPMENTAL BIOLOGY,
1975,
47
(02)
: 319
-
324
[2]
HUMAN-SERUM ALPHA-L-FUCOSIDASE
ALHADEFF, JA
论文数:
0
引用数:
0
h-index:
0
ALHADEFF, JA
JANOWSKY, AJ
论文数:
0
引用数:
0
h-index:
0
JANOWSKY, AJ
[J].
CLINICA CHIMICA ACTA,
1978,
82
(1-2)
: 133
-
140
[3]
ELECTROPHORETIC FORMS OF HUMAN LIVER ALPHA-L-FUCOSIDASE AND THEIR RELATIONSHIP TO FUCOSIDOSIS (MUCOPOLYSACCHARIDOSIS F)
ALHADEFF, JA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
ALHADEFF, JA
MILLER, AL
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
MILLER, AL
WENGER, DA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
WENGER, DA
OBRIEN, JS
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
OBRIEN, JS
[J].
CLINICA CHIMICA ACTA,
1974,
57
(03)
: 307
-
313
[4]
ALHADEFF JA, 1975, J BIOL CHEM, V250, P7106
[5]
ALHADEFF JA, 1978, MOL CELL BIOCHEM, V19, P171
[6]
ALHADEFF JA, 1977, PRACTICAL ENZYMOLOGY, P247
[7]
FUCOSIDOSIS - DETECTION OF CARRIER STATE IN PERIPHERAL-BLOOD LEUKOCYTES
BERATIS, NG
论文数:
0
引用数:
0
h-index:
0
机构:
CITY UNIV NEW YORK, MT SINAI SCH MED, DEPT PEDIAT, DIV MED GENET, NEW YORK, NY 10000 USA
BERATIS, NG
TURNER, BM
论文数:
0
引用数:
0
h-index:
0
机构:
CITY UNIV NEW YORK, MT SINAI SCH MED, DEPT PEDIAT, DIV MED GENET, NEW YORK, NY 10000 USA
TURNER, BM
HIRSCHHORN, K
论文数:
0
引用数:
0
h-index:
0
机构:
CITY UNIV NEW YORK, MT SINAI SCH MED, DEPT PEDIAT, DIV MED GENET, NEW YORK, NY 10000 USA
HIRSCHHORN, K
[J].
JOURNAL OF PEDIATRICS,
1975,
87
(06)
: 1193
-
1198
[8]
FUCOSIDOSIS
DURAND, P
论文数:
0
引用数:
0
h-index:
0
机构:
Third Department of Pediatrics, G. Gaslini Hospital, Genoa
DURAND, P
BORRONE, C
论文数:
0
引用数:
0
h-index:
0
机构:
Third Department of Pediatrics, G. Gaslini Hospital, Genoa
BORRONE, C
DELLACEL.G
论文数:
0
引用数:
0
h-index:
0
机构:
Third Department of Pediatrics, G. Gaslini Hospital, Genoa
DELLACEL.G
[J].
JOURNAL OF PEDIATRICS,
1969,
75
(04)
: 665
-
&
[9]
FUNCTION OF CARBOHYDRATE MOIETY AND ALTERATION OF CARBOHYDRATE-COMPOSITION IN HUMAN ALKALINE-PHOSPHATASE ISOENZYMES
KOMODA, T
论文数:
0
引用数:
0
h-index:
0
KOMODA, T
SAKAGISHI, Y
论文数:
0
引用数:
0
h-index:
0
SAKAGISHI, Y
[J].
BIOCHIMICA ET BIOPHYSICA ACTA,
1978,
523
(02)
: 395
-
406
[10]
The determination of enzyme dissociation constants
Lineweaver, H
论文数:
0
引用数:
0
h-index:
0
机构:
Bur Chem & Soils, Fertilizer Invest Unit, US Dept Agr, Washington, DC USA
Bur Chem & Soils, Fertilizer Invest Unit, US Dept Agr, Washington, DC USA
Lineweaver, H
Burk, D
论文数:
0
引用数:
0
h-index:
0
机构:
Bur Chem & Soils, Fertilizer Invest Unit, US Dept Agr, Washington, DC USA
Bur Chem & Soils, Fertilizer Invest Unit, US Dept Agr, Washington, DC USA
Burk, D
[J].
JOURNAL OF THE AMERICAN CHEMICAL SOCIETY,
1934,
56
: 658
-
666
←
1
2
→
共 16 条
[1]
ISOENZYME PATTERNS OF HUMAN LIVER ALPHA-L-FUCOSIDASE DURING DEVELOPMENT
ALHADEFF, JA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
ALHADEFF, JA
TENNANT, L
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
TENNANT, L
OBRIEN, JS
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
OBRIEN, JS
[J].
DEVELOPMENTAL BIOLOGY,
1975,
47
(02)
: 319
-
324
[2]
HUMAN-SERUM ALPHA-L-FUCOSIDASE
ALHADEFF, JA
论文数:
0
引用数:
0
h-index:
0
ALHADEFF, JA
JANOWSKY, AJ
论文数:
0
引用数:
0
h-index:
0
JANOWSKY, AJ
[J].
CLINICA CHIMICA ACTA,
1978,
82
(1-2)
: 133
-
140
[3]
ELECTROPHORETIC FORMS OF HUMAN LIVER ALPHA-L-FUCOSIDASE AND THEIR RELATIONSHIP TO FUCOSIDOSIS (MUCOPOLYSACCHARIDOSIS F)
ALHADEFF, JA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
ALHADEFF, JA
MILLER, AL
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
MILLER, AL
WENGER, DA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
WENGER, DA
OBRIEN, JS
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF,SAN DIEGO,SCH MED,DEPT NEUROSCI,LA JOLLA,CA 92037
OBRIEN, JS
[J].
CLINICA CHIMICA ACTA,
1974,
57
(03)
: 307
-
313
[4]
ALHADEFF JA, 1975, J BIOL CHEM, V250, P7106
[5]
ALHADEFF JA, 1978, MOL CELL BIOCHEM, V19, P171
[6]
ALHADEFF JA, 1977, PRACTICAL ENZYMOLOGY, P247
[7]
FUCOSIDOSIS - DETECTION OF CARRIER STATE IN PERIPHERAL-BLOOD LEUKOCYTES
BERATIS, NG
论文数:
0
引用数:
0
h-index:
0
机构:
CITY UNIV NEW YORK, MT SINAI SCH MED, DEPT PEDIAT, DIV MED GENET, NEW YORK, NY 10000 USA
BERATIS, NG
TURNER, BM
论文数:
0
引用数:
0
h-index:
0
机构:
CITY UNIV NEW YORK, MT SINAI SCH MED, DEPT PEDIAT, DIV MED GENET, NEW YORK, NY 10000 USA
TURNER, BM
HIRSCHHORN, K
论文数:
0
引用数:
0
h-index:
0
机构:
CITY UNIV NEW YORK, MT SINAI SCH MED, DEPT PEDIAT, DIV MED GENET, NEW YORK, NY 10000 USA
HIRSCHHORN, K
[J].
JOURNAL OF PEDIATRICS,
1975,
87
(06)
: 1193
-
1198
[8]
FUCOSIDOSIS
DURAND, P
论文数:
0
引用数:
0
h-index:
0
机构:
Third Department of Pediatrics, G. Gaslini Hospital, Genoa
DURAND, P
BORRONE, C
论文数:
0
引用数:
0
h-index:
0
机构:
Third Department of Pediatrics, G. Gaslini Hospital, Genoa
BORRONE, C
DELLACEL.G
论文数:
0
引用数:
0
h-index:
0
机构:
Third Department of Pediatrics, G. Gaslini Hospital, Genoa
DELLACEL.G
[J].
JOURNAL OF PEDIATRICS,
1969,
75
(04)
: 665
-
&
[9]
FUNCTION OF CARBOHYDRATE MOIETY AND ALTERATION OF CARBOHYDRATE-COMPOSITION IN HUMAN ALKALINE-PHOSPHATASE ISOENZYMES
KOMODA, T
论文数:
0
引用数:
0
h-index:
0
KOMODA, T
SAKAGISHI, Y
论文数:
0
引用数:
0
h-index:
0
SAKAGISHI, Y
[J].
BIOCHIMICA ET BIOPHYSICA ACTA,
1978,
523
(02)
: 395
-
406
[10]
The determination of enzyme dissociation constants
Lineweaver, H
论文数:
0
引用数:
0
h-index:
0
机构:
Bur Chem & Soils, Fertilizer Invest Unit, US Dept Agr, Washington, DC USA
Bur Chem & Soils, Fertilizer Invest Unit, US Dept Agr, Washington, DC USA
Lineweaver, H
Burk, D
论文数:
0
引用数:
0
h-index:
0
机构:
Bur Chem & Soils, Fertilizer Invest Unit, US Dept Agr, Washington, DC USA
Bur Chem & Soils, Fertilizer Invest Unit, US Dept Agr, Washington, DC USA
Burk, D
[J].
JOURNAL OF THE AMERICAN CHEMICAL SOCIETY,
1934,
56
: 658
-
666
←
1
2
→