PURINOGENIC IMMUNODEFICIENCY DISEASES - CLINICAL-FEATURES AND MOLECULAR MECHANISMS

被引:76
作者
MITCHELL, BS [1 ]
KELLEY, WN [1 ]
机构
[1] UNIV MICHIGAN, SIMPSON MEM INST, ANN ARBOR, MI 48109 USA
关键词
D O I
10.7326/0003-4819-92-6-826
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:826 / 831
页数:6
相关论文
共 92 条
[1]   HEREDITARY SEVERE COMBINED IMMUNODEFICIENCY AND ADENOSINE DEAMINASE DEFICIENCY [J].
ACKERET, C ;
PLUSS, HJ ;
HITZIG, WH .
PEDIATRIC RESEARCH, 1976, 10 (01) :67-70
[2]  
AGARWAL RP, 1979, BIOCHEM PHARMACOL, V26, P259
[3]  
BIGGAR WD, 1978, J PEDIATR-US, V92, P354
[4]  
BJURSELL G, 1973, J BIOL CHEM, V248, P3904
[5]   MODULATION OF INFLAMMATION AND IMMUNITY BY CYCLIC-AMP [J].
BOURNE, HR ;
LICHTENSTEIN, LM ;
MELMON, KL ;
HENNEY, CS ;
WEINSTEIN, Y ;
SHEARER, GM .
SCIENCE, 1974, 184 (4132) :19-28
[6]  
CARAPELLADELUCA E, 1978, J PEDIATR-US, V93, P1000
[7]  
CARSON DA, 1980, J IMMUNOL, V124, P8
[8]  
CARSON DA, 1978, J IMMUNOL, V121, P1726
[9]   BIOCHEMICAL BASIS FOR THE ENHANCED TOXICITY OF DEOXYRIBONUCLEOSIDES TOWARD MALIGNANT HUMAN T-CELL LINES [J].
CARSON, DA ;
KAYE, J ;
MATSUMOTO, S ;
SEEGMILLER, JE ;
THOMPSON, L .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1979, 76 (05) :2430-2433
[10]   LYMPHO-SPECIFIC TOXICITY IN ADENOSINE-DEAMINASE DEFICIENCY AND PURINE NUCLEOSIDE PHOSPHORYLASE DEFICIENCY - POSSIBLE ROLE OF NUCLEOSIDE KINASE(S) [J].
CARSON, DA ;
KAYE, J ;
SEEGMILLER, JE .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1977, 74 (12) :5677-5681