ANIMAL-MODELS OF DUCHENNE AND BECKER MUSCULAR-DYSTROPHY

被引:45
作者
COOPER, BJ
机构
关键词
D O I
10.1093/oxfordjournals.bmb.a072353
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:703 / 718
页数:16
相关论文
共 54 条
[21]   DISTRIBUTION OF FREEZE-FRACTURE PARTICLE SIZES IN DUCHENNE MUSCLE PLASMA-MEMBRANE [J].
FISCHBECK, KH ;
BONILLA, E ;
SCHOTLAND, DL .
NEUROLOGY, 1984, 34 (04) :534-535
[22]   PATHOLOGY OF HEART IN PROGRESSIVE MUSCULAR-DYSTROPHY - EPIMYOCARDIAL FIBROSIS [J].
FRANKEL, KA ;
ROSSER, RJ .
HUMAN PATHOLOGY, 1976, 7 (04) :375-386
[23]   SERUM CK, CALCIUM, MAGNESIUM, AND OXIDATIVE-PHOSPHORYLATION IN MDX MOUSE MUSCULAR-DYSTROPHY [J].
GLESBY, MJ ;
ROSENMANN, E ;
NYLEN, EG ;
WROGEMANN, K .
MUSCLE & NERVE, 1988, 11 (08) :852-856
[24]   LOCALIZATION OF THE REGION HOMOLOGOUS TO THE DUCHENNE MUSCULAR-DYSTROPHY LOCUS ON THE MOUSE X-CHROMOSOME [J].
HEILIG, R ;
LEMAIRE, C ;
MANDEL, JL ;
DANDOLO, L ;
AMAR, L ;
AVNER, P .
NATURE, 1987, 328 (6126) :168-170
[25]   DYSTROPHIN - THE PROTEIN PRODUCT OF THE DUCHENNE MUSCULAR-DYSTROPHY LOCUS [J].
HOFFMAN, EP ;
BROWN, RH ;
KUNKEL, LM .
CELL, 1987, 51 (06) :919-928
[26]   CONSERVATION OF THE DUCHENNE MUSCULAR-DYSTROPHY GENE IN MICE AND HUMANS [J].
HOFFMAN, EP ;
MONACO, AP ;
FEENER, CC ;
KUNKEL, LM .
SCIENCE, 1987, 238 (4825) :347-350
[27]   MEMBRANE ABNORMALITIES IN DUCHENNE MUSCULAR-DYSTROPHY [J].
JONES, GE ;
WITKOWSKI, JA .
JOURNAL OF THE NEUROLOGICAL SCIENCES, 1983, 58 (02) :159-174
[28]   SMALL-CALIBER SKELETAL-MUSCLE FIBERS DO NOT SUFFER NECROSIS IN MDX MOUSE DYSTROPHY [J].
KARPATI, G ;
CARPENTER, S ;
PRESCOTT, S .
MUSCLE & NERVE, 1988, 11 (08) :795-803
[29]   COMPLETE CLONING OF THE DUCHENNE MUSCULAR-DYSTROPHY (DMD) CDNA AND PRELIMINARY GENOMIC ORGANIZATION OF THE DMD GENE IN NORMAL AND AFFECTED INDIVIDUALS [J].
KOENIG, M ;
HOFFMAN, EP ;
BERTELSON, CJ ;
MONACO, AP ;
FEENER, C ;
KUNKEL, LM .
CELL, 1987, 50 (03) :509-517
[30]   MUSCULAR-DYSTROPHY IN A LITTER OF GOLDEN RETRIEVER DOGS [J].
KORNEGAY, JN ;
TULER, SM ;
MILLER, DM ;
LEVESQUE, DC .
MUSCLE & NERVE, 1988, 11 (10) :1056-1064