ANTI-MULLERIAN HORMONE AND SERTOLI-CELL FUNCTION

被引:24
作者
JOSSO, N
机构
关键词
MULLERIAN INHIBITING SUBSTANCE; MULLERIAN INHIBITING FACTOR; SERTOLI CELLS; INTERSEX STATES; ANORCHIA; PERSISTENT MULLERIAN DUCT SYNDROME;
D O I
10.1159/000182602
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Anti-Mullerian hormone (AMH) is a glycoprotein that is produced by immature Sertoli cells and is responsible for the regression of Mullerian ducts in male fetuses. It is a useful marker of testicular function in children, when anorchia is suspected and in intersex states. In the persistent Mullerian duct syndrome, both AMH-positive and AMH-negative forms have been reported. In three cases of the latter, a mutation of the AMH gene is thought to have been responsible for the condition.
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页码:72 / 76
页数:5
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