THE INTERACTION OF ALPHA-THALASSEMIA AND HOMOZYGOUS SICKLE-CELL DISEASE

被引:289
作者
HIGGS, DR
ALDRIDGE, BE
LAMB, J
CLEGG, JB
WEATHERALL, DJ
HAYES, RJ
GRANDISON, Y
LOWRIE, Y
MASON, KP
SERJEANT, BE
SERJEANT, GR
机构
[1] UNIV W INDIES,MED RES COUNCIL LABS,KINGSTON,JAMAICA
[2] UNIV OXFORD,JOHN RADCLIFFE HOSP,NUFFIELD DEPT CLIN MED,MED RES COUNCIL MOLEC HAEMATOL UNIT,OXFORD OX3 9DU,ENGLAND
[3] UNIV LONDON LONDON SCH HYG & TROP MED,TROP EPIDEMIOL UNIT,LONDON WC1E 7HT,ENGLAND
关键词
D O I
10.1056/NEJM198206173062402
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:1441 / 1446
页数:6
相关论文
共 29 条
[21]   ERYTHROCYTE HB-S CONCENTRATION - IMPORTANT FACTOR IN LOW OXYGEN AFFINITY OF BLOOD IN SICKLE-CELL ANEMIA [J].
SEAKINS, M ;
GIBBS, WN ;
MILNER, PF ;
BERTLES, JF .
JOURNAL OF CLINICAL INVESTIGATION, 1973, 52 (02) :422-432
[22]  
SERJEANT GR, 1975, CLIN HAEMATOL, V4, P109
[23]   COMPARISON OF SICKLE CELL BETA-0 THALASSEMIA WITH HOMOZYGOUS SICKLE-CELL DISEASE [J].
SERJEANT, GR ;
SOMMEREUX, A ;
STEVENSON, M ;
MASON, K ;
SERJEANT, BE .
BRITISH JOURNAL OF HAEMATOLOGY, 1979, 41 (01) :83-93
[24]   IRREVERSIBLY SICKLED CELL - A DETERMINANT OF HAEMOLYSIS IN SICKLE CELL ANAEMIA [J].
SERJEANT, GR ;
SERJEANT, BE ;
MILNER, PF .
BRITISH JOURNAL OF HAEMATOLOGY, 1969, 17 (06) :527-&
[25]  
SERJEANT GR, 1980, RED CELL, P781
[26]  
SEWELL A, 1978, RED CELL, P93
[27]   CLINICAL LONGITUDINAL STANDARDS FOR HEIGHT, WEIGHT, HEIGHT VELOCITY, WEIGHT VELOCITY, AND STAGES OF PUBERTY [J].
TANNER, JM ;
WHITEHOUSE, RH .
ARCHIVES OF DISEASE IN CHILDHOOD, 1976, 51 (03) :170-179
[28]   BENIGN OBSTETRIC HISTORY IN WOMEN WITH SICKLE-CELL ANEMIA ASSOCIATED WITH ALPHA-THALASSEMIA [J].
VANENK, A ;
WHITE, JM ;
LEHMANN, H ;
LANG, A .
BRITISH MEDICAL JOURNAL, 1972, 4 (5839) :524-&
[29]   A NEW SICKLING DISORDER RESULTING FROM INTERACTION OF GENES FOR HAEMOGLOBIN-S AND ALPHA-THALASSAEMIA [J].
WEATHERALL, DJ ;
CLEGG, JB ;
BLANKSON, J ;
MCNEIL, JR .
BRITISH JOURNAL OF HAEMATOLOGY, 1969, 17 (06) :517-+