PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA TYPE-III - LACK OF AN ERYTHROCYTE-MEMBRANE PROTEIN RESTRICTING THE LYSIS BY C5B-9

被引:103
作者
HANSCH, GM
SCHONERMARK, S
ROELCKE, D
机构
关键词
D O I
10.1172/JCI113065
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:7 / 12
页数:6
相关论文
共 38 条
[11]   MECHANISMS OF IMMUNE LYSIS OF RED BLOOD-CELLS IN-VITRO .1. PAROXYSMAL NOCTURNAL HEMOGLOBINURIA CELLS [J].
LOGUE, GL ;
ROSSE, WF ;
ADAMS, JP .
JOURNAL OF CLINICAL INVESTIGATION, 1973, 52 (05) :1129-1137
[12]  
LUCIUS R, 1983, TROPENMED PARASITOL, V34, P75
[13]  
MAYER MM, 1961, EXPT IMMUNOCHEMISTRY, P111
[14]   INHIBITION OF COMPLEMENT ACTIVATION ON THE SURFACE OF CELLS AFTER INCORPORATION OF DECAY-ACCELERATING FACTOR (DAF) INTO THEIR MEMBRANES [J].
MEDOF, ME ;
KINOSHITA, T ;
NUSSENZWEIG, V .
JOURNAL OF EXPERIMENTAL MEDICINE, 1984, 160 (05) :1558-1578
[15]  
MONAHAN JB, 1980, J BIOL CHEM, V255, P579
[16]  
NICHOLSONWELLER A, 1982, J IMMUNOL, V129, P184
[17]   AFFECTED ERYTHROCYTES OF PATIENTS WITH PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA ARE DEFICIENT IN THE COMPLEMENT REGULATORY PROTEIN, DECAY ACCELERATING FACTOR [J].
NICHOLSONWELLER, A ;
MARCH, JP ;
ROSENFELD, SI ;
AUSTEN, KF .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1983, 80 (16) :5066-5070
[18]   COMPLEMENT LYSIS OF HUMAN-ERYTHROCYTES - DIFFERING SUSCEPTIBILITY OF 2 TYPES OF PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA CELLS TO C5B-9 [J].
PACKMAN, CH ;
ROSENFELD, SI ;
JENKINS, DE ;
THIEM, PA ;
LEDDY, JP .
JOURNAL OF CLINICAL INVESTIGATION, 1979, 64 (02) :428-433
[19]  
PACKMAN CH, 1980, J IMMUNOL, V124, P2818
[20]   PAROXYSMAL-NOCTURNAL HEMOGLOBINURIA - DEFICIENCY IN FACTOR H-LIKE FUNCTIONS OF THE ABNORMAL ERYTHROCYTES [J].
PANGBURN, MK ;
SCHREIBER, RD ;
TROMBOLD, JS ;
MULLEREBERHARD, HJ .
JOURNAL OF EXPERIMENTAL MEDICINE, 1983, 157 (06) :1971-1980