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DYSFUNCTIONAL C1BAR-INHIBITOR(AT), ISOLATED FROM A TYPE-II HEREDITARY-ANGIO-EDEMA PLASMA, CONTAINS A P1 REACTIVE CENTER (ARG-444-]HIS) MUTATION
被引:68
作者
:
AULAK, KS
论文数:
0
引用数:
0
h-index:
0
机构:
MRC, MIP UNIT, HILLS RD, CAMBRIDGE CB2 2QH, ENGLAND
AULAK, KS
PEMBERTON, PA
论文数:
0
引用数:
0
h-index:
0
机构:
MRC, MIP UNIT, HILLS RD, CAMBRIDGE CB2 2QH, ENGLAND
PEMBERTON, PA
ROSEN, FS
论文数:
0
引用数:
0
h-index:
0
机构:
MRC, MIP UNIT, HILLS RD, CAMBRIDGE CB2 2QH, ENGLAND
ROSEN, FS
CARRELL, RW
论文数:
0
引用数:
0
h-index:
0
机构:
MRC, MIP UNIT, HILLS RD, CAMBRIDGE CB2 2QH, ENGLAND
CARRELL, RW
LACHMANN, PJ
论文数:
0
引用数:
0
h-index:
0
机构:
MRC, MIP UNIT, HILLS RD, CAMBRIDGE CB2 2QH, ENGLAND
LACHMANN, PJ
HARRISON, RA
论文数:
0
引用数:
0
h-index:
0
机构:
MRC, MIP UNIT, HILLS RD, CAMBRIDGE CB2 2QH, ENGLAND
HARRISON, RA
机构
:
[1]
MRC, MIP UNIT, HILLS RD, CAMBRIDGE CB2 2QH, ENGLAND
[2]
UNIV CAMBRIDGE, SCH MED, DEPT HAEMATOL MED, CAMBRIDGE CB2 2QH, ENGLAND
[3]
CTR BLOOD RES, BOSTON, MA 02115 USA
来源
:
BIOCHEMICAL JOURNAL
|
1988年
/ 253卷
/ 02期
基金
:
英国惠康基金;
关键词
:
D O I
:
10.1042/bj2530615
中图分类号
:
Q5 [生物化学];
Q7 [分子生物学];
学科分类号
:
071010 ;
081704 ;
摘要
:
引用
收藏
页码:615 / 618
页数:4
相关论文
共 31 条
[1]
HUMAN C1BAR INHIBITOR - PRIMARY STRUCTURE, CDNA CLONING, AND CHROMOSOMAL LOCALIZATION
BOCK, SC
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
BOCK, SC
SKRIVER, K
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
SKRIVER, K
NIELSEN, E
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
NIELSEN, E
THOGERSEN, HC
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
THOGERSEN, HC
WIMAN, B
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
WIMAN, B
DONALDSON, VH
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
DONALDSON, VH
EDDY, RL
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
EDDY, RL
MARRINAN, J
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
MARRINAN, J
RADZIEJEWSKA, E
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
RADZIEJEWSKA, E
HUBER, R
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
HUBER, R
SHOWS, TB
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
SHOWS, TB
MAGNUSSON, S
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
MAGNUSSON, S
[J].
BIOCHEMISTRY,
1986,
25
(15)
: 4292
-
4301
[2]
PLAKALBUMIN, ALPHA-1-ANTITRYPSIN, ANTITHROMBIN AND THE MECHANISM OF INFLAMMATORY THROMBOSIS
CARRELL, RW
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CAMBRIDGE,SCH MED,MRC,MOLEC BIOL LAB,CAMBRIDGE CB2 2QH,ENGLAND
CARRELL, RW
OWEN, MC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CAMBRIDGE,SCH MED,MRC,MOLEC BIOL LAB,CAMBRIDGE CB2 2QH,ENGLAND
OWEN, MC
[J].
NATURE,
1985,
317
(6039)
: 730
-
732
[3]
CARRELL RW, 1986, PROTEINASE INHIBITOR, pCH12
[4]
CULLMANN W, 1986, PROG ALLERGY, V39, P311
[5]
CURD JG, 1981, CLIN EXP IMMUNOL, V45, P261
[6]
INACTIVATION OF FACTOR-XII ACTIVE FRAGMENT IN NORMAL PLASMA - PREDOMINANT ROLE OF C1BAR-INHIBITOR
DEAGOSTINI, A
论文数:
0
引用数:
0
h-index:
0
机构:
CATHOLIC UNIV LEUVEN, CTR THROMBOSIS & VASC RES, DEPT MED RES, B-3000 LOUVAIN, BELGIUM
DEAGOSTINI, A
LIJNEN, HR
论文数:
0
引用数:
0
h-index:
0
机构:
CATHOLIC UNIV LEUVEN, CTR THROMBOSIS & VASC RES, DEPT MED RES, B-3000 LOUVAIN, BELGIUM
LIJNEN, HR
PIXLEY, RA
论文数:
0
引用数:
0
h-index:
0
机构:
CATHOLIC UNIV LEUVEN, CTR THROMBOSIS & VASC RES, DEPT MED RES, B-3000 LOUVAIN, BELGIUM
PIXLEY, RA
COLMAN, RW
论文数:
0
引用数:
0
h-index:
0
机构:
CATHOLIC UNIV LEUVEN, CTR THROMBOSIS & VASC RES, DEPT MED RES, B-3000 LOUVAIN, BELGIUM
COLMAN, RW
SCHAPIRA, M
论文数:
0
引用数:
0
h-index:
0
机构:
CATHOLIC UNIV LEUVEN, CTR THROMBOSIS & VASC RES, DEPT MED RES, B-3000 LOUVAIN, BELGIUM
SCHAPIRA, M
[J].
JOURNAL OF CLINICAL INVESTIGATION,
1984,
73
(06)
: 1542
-
1549
[7]
A BIOCHEMICAL ABNORMALITY IN HEREDITARY ANGIONEUROTIC EDEMA - ABSENCE OF SERUM INHIBITOR OF C 1-ESTERASE
DONALDSON, VH
论文数:
0
引用数:
0
h-index:
0
DONALDSON, VH
EVANS, RR
论文数:
0
引用数:
0
h-index:
0
EVANS, RR
[J].
AMERICAN JOURNAL OF MEDICINE,
1963,
35
(01)
: 37
-
+
[8]
VARIABILITY IN PURIFIED DYSFUNCTIONAL C1-INHIBITOR PROTEINS FROM PATIENTS WITH HEREDITARY ANGIONEUROTIC-EDEMA - FUNCTIONAL AND ANALYTICAL GEL STUDIES
DONALDSON, VH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229
DONALDSON, VH
HARRISON, RA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229
HARRISON, RA
ROSEN, FS
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229
ROSEN, FS
BING, DH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229
BING, DH
KINDNESS, G
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229
KINDNESS, G
CANAR, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229
CANAR, J
WAGNER, CJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229
WAGNER, CJ
AWAD, S
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229
AWAD, S
[J].
JOURNAL OF CLINICAL INVESTIGATION,
1985,
75
(01)
: 124
-
132
[9]
DONALDSON VH, 1987, BLOOD, V69, P1096
[10]
ERDJUMENT H, 1987, J BIOL CHEM, V262, P13381
←
1
2
3
4
→
共 31 条
[1]
HUMAN C1BAR INHIBITOR - PRIMARY STRUCTURE, CDNA CLONING, AND CHROMOSOMAL LOCALIZATION
BOCK, SC
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
BOCK, SC
SKRIVER, K
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
SKRIVER, K
NIELSEN, E
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
NIELSEN, E
THOGERSEN, HC
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
THOGERSEN, HC
WIMAN, B
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
WIMAN, B
DONALDSON, VH
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
DONALDSON, VH
EDDY, RL
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
EDDY, RL
MARRINAN, J
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
MARRINAN, J
RADZIEJEWSKA, E
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
RADZIEJEWSKA, E
HUBER, R
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
HUBER, R
SHOWS, TB
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
SHOWS, TB
MAGNUSSON, S
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,DEPT MOLEC BIOL,DK-8000 AARHUS C,DENMARK
MAGNUSSON, S
[J].
BIOCHEMISTRY,
1986,
25
(15)
: 4292
-
4301
[2]
PLAKALBUMIN, ALPHA-1-ANTITRYPSIN, ANTITHROMBIN AND THE MECHANISM OF INFLAMMATORY THROMBOSIS
CARRELL, RW
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CAMBRIDGE,SCH MED,MRC,MOLEC BIOL LAB,CAMBRIDGE CB2 2QH,ENGLAND
CARRELL, RW
OWEN, MC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CAMBRIDGE,SCH MED,MRC,MOLEC BIOL LAB,CAMBRIDGE CB2 2QH,ENGLAND
OWEN, MC
[J].
NATURE,
1985,
317
(6039)
: 730
-
732
[3]
CARRELL RW, 1986, PROTEINASE INHIBITOR, pCH12
[4]
CULLMANN W, 1986, PROG ALLERGY, V39, P311
[5]
CURD JG, 1981, CLIN EXP IMMUNOL, V45, P261
[6]
INACTIVATION OF FACTOR-XII ACTIVE FRAGMENT IN NORMAL PLASMA - PREDOMINANT ROLE OF C1BAR-INHIBITOR
DEAGOSTINI, A
论文数:
0
引用数:
0
h-index:
0
机构:
CATHOLIC UNIV LEUVEN, CTR THROMBOSIS & VASC RES, DEPT MED RES, B-3000 LOUVAIN, BELGIUM
DEAGOSTINI, A
LIJNEN, HR
论文数:
0
引用数:
0
h-index:
0
机构:
CATHOLIC UNIV LEUVEN, CTR THROMBOSIS & VASC RES, DEPT MED RES, B-3000 LOUVAIN, BELGIUM
LIJNEN, HR
PIXLEY, RA
论文数:
0
引用数:
0
h-index:
0
机构:
CATHOLIC UNIV LEUVEN, CTR THROMBOSIS & VASC RES, DEPT MED RES, B-3000 LOUVAIN, BELGIUM
PIXLEY, RA
COLMAN, RW
论文数:
0
引用数:
0
h-index:
0
机构:
CATHOLIC UNIV LEUVEN, CTR THROMBOSIS & VASC RES, DEPT MED RES, B-3000 LOUVAIN, BELGIUM
COLMAN, RW
SCHAPIRA, M
论文数:
0
引用数:
0
h-index:
0
机构:
CATHOLIC UNIV LEUVEN, CTR THROMBOSIS & VASC RES, DEPT MED RES, B-3000 LOUVAIN, BELGIUM
SCHAPIRA, M
[J].
JOURNAL OF CLINICAL INVESTIGATION,
1984,
73
(06)
: 1542
-
1549
[7]
A BIOCHEMICAL ABNORMALITY IN HEREDITARY ANGIONEUROTIC EDEMA - ABSENCE OF SERUM INHIBITOR OF C 1-ESTERASE
DONALDSON, VH
论文数:
0
引用数:
0
h-index:
0
DONALDSON, VH
EVANS, RR
论文数:
0
引用数:
0
h-index:
0
EVANS, RR
[J].
AMERICAN JOURNAL OF MEDICINE,
1963,
35
(01)
: 37
-
+
[8]
VARIABILITY IN PURIFIED DYSFUNCTIONAL C1-INHIBITOR PROTEINS FROM PATIENTS WITH HEREDITARY ANGIONEUROTIC-EDEMA - FUNCTIONAL AND ANALYTICAL GEL STUDIES
DONALDSON, VH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229
DONALDSON, VH
HARRISON, RA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229
HARRISON, RA
ROSEN, FS
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229
ROSEN, FS
BING, DH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229
BING, DH
KINDNESS, G
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229
KINDNESS, G
CANAR, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229
CANAR, J
WAGNER, CJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229
WAGNER, CJ
AWAD, S
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CINCINNATI,CHILDRENS HOSP RES FDN,COLL MED,DEPT PEDIAT,CINCINNATI,OH 45229
AWAD, S
[J].
JOURNAL OF CLINICAL INVESTIGATION,
1985,
75
(01)
: 124
-
132
[9]
DONALDSON VH, 1987, BLOOD, V69, P1096
[10]
ERDJUMENT H, 1987, J BIOL CHEM, V262, P13381
←
1
2
3
4
→