METABOLISM AND CLINICAL RELEVANCE OF KETO ACID ANALOGS OF ESSENTIAL AMINO-ACIDS

被引:20
作者
RICHARDS, P [1 ]
机构
[1] ST GEORGES MED SCH,LONDON SW17 0RE,ENGLAND
来源
CLINICAL SCIENCE AND MOLECULAR MEDICINE | 1978年 / 54卷 / 06期
关键词
D O I
10.1042/cs0540589
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:589 / 593
页数:5
相关论文
共 49 条
[1]   TREATMENT OF CARBAMYL-PHOSPHATE SYNTHETASE DEFICIENCY WITH KETO ANALOGUES OF ESSENTIAL AMINO-ACIDS [J].
BATSHAW, M ;
BRUSILOW, S ;
WALSER, M .
NEW ENGLAND JOURNAL OF MEDICINE, 1975, 292 (21) :1085-1090
[2]  
BATSHAW ML, 1976, PEDIATRICS, V58, P227
[3]  
Bergstrom J, 1975, Clin Nephrol, V3, P187
[4]  
CHAN W, J NUTRITION
[5]   UTILIZATION OF ALPHA-KETO AND ALPHA-HYDROXY ANALOGS OF VALINE BY GROWING RAT [J].
CHAWLA, RK ;
RUDMAN, D .
JOURNAL OF CLINICAL INVESTIGATION, 1974, 54 (02) :271-277
[6]   EFFICIENCY OF ALPHA-KETOISOCAPROIC ACID AS A SUBSTITUTE FOR LEUCINE IN DIET OF GROWING RAT [J].
CHAWLA, RK ;
STACKHOUSE, WJ ;
WADSWORTH, AD .
JOURNAL OF NUTRITION, 1975, 105 (06) :798-803
[7]   EFFECTS OF SUBSTITUTION OF METHIONINE, LEUCINE, PHENYLALANINE, OR VALINE BY THEIR ALPHA-HYDROXY ANALOGS IN DIET OF RATS [J].
CHOW, KW ;
WALSER, M .
JOURNAL OF NUTRITION, 1975, 105 (03) :372-378
[8]   SUBSTITUTION OF 5 ESSENTIAL AMINO-ACIDS BY THEIR ALPHA-KETO ANALOGS IN DIET OF RATS [J].
CHOW, KW ;
WALSER, M .
JOURNAL OF NUTRITION, 1974, 104 (09) :1208-1214
[9]   USE OF AMINO-ACID PRECURSORS IN NITROGEN-ACCUMULATION DISEASES [J].
CLOSE, JH .
NEW ENGLAND JOURNAL OF MEDICINE, 1974, 290 (12) :663-667
[10]  
ELL S, AM J CLIN NUTRITION