共 27 条
[1]
BOWDEN JA, 1968, J BIOL CHEM, V243, P3526
[2]
CONNELLY JL, 1968, J BIOL CHEM, V243, P1198
[3]
DICKINSON JC, 1965, PEDIATRICS, V36, P2
[4]
CLASSICAL MAPLE SYRUP URINE DISEASE - COFACTOR RESISTANCE
[J].
METABOLISM-CLINICAL AND EXPERIMENTAL,
1972, 21 (10)
:929-&
[5]
ELSAS LJ, 1973, PEDIATR RES, V7, P382
[7]
POSTMORTEM DIAGNOSIS OF METABOLIC DISORDERS - FINDING OF MAPLE SYRUP URINE DISEASE IN A CASE OF SUDDEN AND UNEXPECTED DEATH IN INFANCY
[J].
AMERICAN JOURNAL OF DISEASES OF CHILDREN,
1969, 118 (04)
:649-&
[9]
BRANCHED-CHAIN ALPHA-KETO ACIDS ISOLATED AS OXIME DERIVATIVES - RELATIONSHIP TO CORRESPONDING HYDROXY-ACIDS AND AMINO-ACIDS IN MAPLE SYRUP URINE DISEASE
[J].
METABOLISM-CLINICAL AND EXPERIMENTAL,
1974, 23 (03)
:257-265