I-CELL DISEASE - ISOELECTRIC-FOCUSING, CONCANAVALIN A SEPHAROSE 4B BINDING AND KINETIC-PROPERTIES OF HUMAN LIVER ACID BETA-D-GALACTOSIDASES

被引：18

作者：

MILLER, AL

机构：

来源：

BIOCHIMICA ET BIOPHYSICA ACTA | 1978年 / 522卷 / 01期

关键词：

D O I：

10.1016/0005-2744(78)90333-9

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：174 / 186

页数：13

共 54 条

[1] GEL-FILTRATION BEHAVIOUR OF PROTEINS RELATED TO THEIR MOLECULAR WEIGHTS OVER A WIDE RANGE [J].

ANDREWS, P .

BIOCHEMICAL JOURNAL, 1965, 96 (03) :595-&

[2] PRENATAL DIAGNOSIS AND FETAL PATHOLOGY OF I-CELL DISEASE (MUCOLIPIDOSIS TYPE-2) [J].

AULA, P ;

RAPOLA, J ;

AUTIO, S ;

RAIVIO, K ;

KARJALAINEN, O .

JOURNAL OF PEDIATRICS, 1975, 87 (02) :221-226

[3]

AUTIO S, 1974, DEV MED CHILD NEUROL, V16, P377

[4]

BLANK E, 1974, PEDIATRICS, V54, P797

[5] MUCOLIPIDOSIS-1 - INCREASED SIALIC-ACID CONTENT AND DEFICIENCY OF ANALPHA-N-ACETYLNEURAMINIDASE IN CULTURED FIBROBLASTS [J].

CANTZ, M ;

GEHLER, J ;

SPRANGER, J .

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1977, 74 (02) :732-738

[6]

DENTANDT WR, 1974, J LAB CLIN MED, V83, P403

[7]

FARRIAUX JP, 1976, LILLE MED, V21, P51

[8]

FREE SJ, 1977, J SUPRAMOL STRUCT S1, P319

[9]

HAGLUND H, 1967, SCIENCE TOOLS, V14, P1

[10] ULTRASTRUCTURE OF CULTURED FIBROBLASTS IN I-CELL DISEASE [J].

HANAI, J ;

LEROY, J ;

OBRIEN, JS .

AMERICAN JOURNAL OF DISEASES OF CHILDREN, 1971, 122 (01) :34-&

← 1 2 3 4 5 6 →