ABNORMALITY OF LONG-CHAIN FATTY-ACIDS IN ERYTHROCYTE-MEMBRANE SPHINGOMYELIN FROM PATIENTS WITH ADRENOLEUKODYSTROPHY

被引:104
作者
TSUJI, S [1 ]
SUZUKI, M [1 ]
ARIGA, T [1 ]
SEKINE, M [1 ]
KURIYAMA, M [1 ]
MIYATAKE, T [1 ]
机构
[1] TOKYO METROPOLITAN INST MED SCI,TOKYO 113,JAPAN
关键词
D O I
10.1111/j.1471-4159.1981.tb01698.x
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:1046 / 1049
页数:4
相关论文
共 12 条
  • [1] PREPARATION AND CHEMICAL CHARACTERISTICS OF HEMOGLOBIN-FREE GHOSTS OF HUMAN ERYTHROCYTES
    DODGE, JT
    HANAHAN, DJ
    MITCHELL, C
    [J]. ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1963, 100 (01) : 119 - &
  • [2] FATTY-ACID ABNORMALITY IN ADRENOLEUKODYSTROPHY
    IGARASHI, M
    SCHAUMBURG, HH
    POWERS, J
    KISHIMOTO, Y
    KOLODNY, E
    SUZUKI, K
    [J]. JOURNAL OF NEUROCHEMISTRY, 1976, 26 (04) : 851 - &
  • [3] BRAIN GANGLIOSIDES IN ADRENOLEUKODYSTROPHY
    IGARASHI, M
    BELCHIS, D
    SUZUKI, K
    [J]. JOURNAL OF NEUROCHEMISTRY, 1976, 27 (01) : 327 - &
  • [4] HIGH-CONCENTRATION OF HEXACOSANOATE IN CULTURED SKIN FIBROBLAST LIPIDS FROM ADRENOLEUKODYSTROPHY PATIENTS
    KAWAMURA, N
    MOSER, AB
    MOSER, HW
    OGINO, T
    SUZUKI, K
    SCHAUMBURG, H
    MILUNSKY, A
    MURPHY, J
    KISHIMOTO, Y
    [J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1978, 82 (01) : 114 - 120
  • [5] MEE JML, 1976, ANAL LETT, V9, P1075
  • [6] Miyatake T, 1978, Adv Exp Med Biol, V100, P585
  • [7] ANALYSIS OF BIOGENIC-AMINES AND THEIR METABOLITES BY GAS CHROMATOGRAPHY CHEMICAL IONIZATION MASS-SPECTROMETRY
    MIYAZAKI, H
    HASHIMOTO, Y
    IWANAGA, M
    KUBODERA, T
    [J]. JOURNAL OF CHROMATOGRAPHY, 1974, 99 (NOV6): : 575 - 586
  • [8] NEUROCHEMICAL FINDINGS IN ADRENO-LEUKODYSTROPHY
    RAMSEY, RB
    BANIK, NL
    SCOTT, T
    DAVISON, AN
    [J]. JOURNAL OF THE NEUROLOGICAL SCIENCES, 1976, 29 (2-4) : 277 - 294
  • [9] DETERMINATION OF NEURAMINIDASE-SUSCEPTIBLE AND TOTAL N-ACETYLNEURAMINIC ACID IN CELLS BY SELECTED ION MONITORING
    ROBOZ, J
    SUZUKI, R
    BEKESI, JG
    [J]. ANALYTICAL BIOCHEMISTRY, 1978, 87 (01) : 195 - 205
  • [10] ADRENOLEUKODYSTROPHY - CLINICAL AND PATHOLOGICAL-STUDY OF 17 CASES
    SCHAUMBURG, HH
    POWERS, JM
    RAINE, CS
    SUZUKI, K
    RICHARDSON, EP
    [J]. ARCHIVES OF NEUROLOGY, 1975, 32 (09) : 577 - 591