TREATMENT OF MAPLE SYRUP URINE DISEASE

被引:11
作者
GOODMAN, SI
POLLAK, S
MILES, B
OBRIEN, D
机构
[1] University of Colorado Medical Center, Denver, CO
关键词
D O I
10.1016/S0022-3476(69)80278-7
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
The early management of 3 infants with maple syrup urine disease is described with particular reference to variations in daily requirements for branched-chain amino acids. The use of a new dry base mix consisting of a dextrimaltose-corn oil-mineral mix, an iron-vitamin mix, and an amino acid mix as a formula base has facilitated earlier home management of these patients. © 1969 The C. V. Mosby Company.
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页码:485 / &
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SNYDERMAN SE, 1964, PEDIATRICS, V34, P454
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