POLY-UNSATURATED FATTY-ACID CHANGES SUGGESTING A NEW ENZYMATIC DEFECT IN ZELLWEGER SYNDROME

被引：56

作者：

MARTINEZ, M ^{[1
]}

机构：

[1] AUTONOMOUS UNIV BARCELONA,HOSP INFANTIL VALL HEBRON,SCH MED,E-08035 BARCELONA,SPAIN

来源：

LIPIDS | 1989年 / 24卷 / 04期

关键词：

D O I：

10.1007/BF02535160

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：261 / 265

页数：5

共 25 条

[1] ULTRASTRUCTURAL AND CYTOCHEMICAL DEMONSTRATION OF PEROXISOMES IN CULTURED FIBROBLASTS FROM PATIENTS WITH PEROXISOMAL DEFICIENCY DISORDERS [J].

ARIAS, JA ;

MOSER, AB ;

GOLDFISCHER, SL .

JOURNAL OF CELL BIOLOGY, 1985, 100 (05) :1789-1792

[2]

BROWN FR, 1982, JOHNS HOPKINS MED J, V151, P344

[3] INFLUENCE OF ENVIRONMENTAL MEDIUM ON FATTY-ACID COMPOSITION OF HUMAN-CELLS - LEUKOCYTES AND FIBROBLASTS [J].

DELPLANQUE, B ;

JACOTOT, B .

LIPIDS, 1987, 22 (04) :241-249

[4] POLYPEPTIDE AND PHOSPHOLIPID-COMPOSITION OF THE MEMBRANE OF RAT-LIVER PEROXISOMES - COMPARISON WITH ENDOPLASMIC-RETICULUM AND MITOCHONDRIAL-MEMBRANES [J].

FUJIKI, Y ;

FOWLER, S ;

SHIO, H ;

HUBBARD, AL ;

LAZAROW, PB .

JOURNAL OF CELL BIOLOGY, 1982, 93 (01) :103-110

[5] EFFECTS OF DIETARY FATTY ACIDS ON FATTY ACID COMPOSITION OF BRAIN ETHANOLAMINE PHOSPHOGLYCERIDE - RECIPROCAL REPLACEMENT OF N-6 AND N-3 POLYUNSATURATED FATTY ACIDS [J].

GALLI, C ;

TRZECIAK, HI ;

PAOLETTI, R .

BIOCHIMICA ET BIOPHYSICA ACTA, 1971, 248 (03) :449-&

[6] PEROXISOMAL AND MITOCHONDRIAL DEFECTS IN CEREBRO-HEPATO-RENAL SYNDROME [J].

GOLDFISCHER, S ;

MOORE, CL ;

JOHNSON, AB ;

SPIRO, AJ ;

VALSAMIS, MP ;

WISNIEWSKI, HK ;

RITCH, RH ;

NORTON, WT ;

RAPIN, I ;

GARTNER, LM .

SCIENCE, 1973, 182 (4107) :62-64

[7] SERIAL SECTION ANALYSIS OF MOUSE HEPATIC PEROXISOMES [J].

GORGAS, K .

ANATOMY AND EMBRYOLOGY, 1985, 172 (01) :21-32

[8]

HAJRA AK, 1979, J BIOL CHEM, V254, P896

[9] SEVERE PLASMALOGEN DEFICIENCY IN TISSUES OF INFANTS WITHOUT PEROXISOMES (ZELLWEGER SYNDROME) [J].

HEYMANS, HSA ;

SCHUTGENS, RBH ;

TAN, R ;

VANDENBOSCH, H ;

BORST, P .

NATURE, 1983, 306 (5938) :69-70

[10] TRIGLYCERIDE ACCUMULATION IN CULTURED HUMAN FIBROBLASTS - EFFECTS OF HYPERTRIGLYCERIDEMIC SERUM [J].

HOWARD, BV ;

HOWARD, WJ ;

DELALLERA, M ;

KEFALIDES, NA .

ATHEROSCLEROSIS, 1976, 23 (03) :521-534

← 1 2 3 →