CONGENITAL HYPOPITUITARISM IN FEMALE INFANTS - ITS ASSOCIATION WITH HYPOGLYCEMIA AND HYPO-THYROIDISM

被引:27
作者
KAUSCHANSKY, A
GENEL, M
SMITH, GJW
机构
[1] YALE UNIV,SCH MED,DEPT PEDIAT,PEDIAT ENDOCRINOL SECT,NEW HAVEN,CT 06510
[2] YALE UNIV,SCH MED,DEPT PATHOL,NEW HAVEN,CT 06510
[3] YALE NEW HAVEN HOSP,NEW HAVEN,CT 06504
来源
AMERICAN JOURNAL OF DISEASES OF CHILDREN | 1979年 / 133卷 / 02期
关键词
D O I
10.1001/archpedi.1979.02130020057011
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Congenital hypopituitarism was found in two female infants who had profound hypoglycemia and hypothyroidism. In both infants, death occurred despite recognition of the disorder and institution of appropriate therapy. Autopsy findings showed an absent pituitary gland and sella turcica, with hypoplastic adrenal and thyroid glands, and ovaries in one case, and pituitary gland aplasia with absent thyroid and right adrenal glands plus a hypoplastic left adrenal gland in the other case. © 1979, American Medical Association. All rights reserved.
引用
收藏
页码:165 / 169
页数:5
相关论文
共 31 条
[11]   METABOLIC RESPONSE TO HUMAN GROWTH HORMONE DURING PROLONGED STARVATION [J].
FELIG, P ;
MARLISS, EB ;
CAHILL, GF .
JOURNAL OF CLINICAL INVESTIGATION, 1971, 50 (02) :411-+
[12]   ROLE OF GROWTH-HORMONE AND CORTISONE ON GLUCOSE AND GLUCONEOGENIC SUBSTRATE REGULATION IN FASTED HYPOPITUITARY CHILDREN [J].
HAYMOND, MW ;
KARL, I ;
WELDON, VV ;
PAGLIARA, AS .
JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM, 1976, 42 (05) :846-856
[13]   FAMILIAL HOLOPROSENCEPHALY WITH ENDOCRINE DYSGENESIS [J].
HINTZ, RL ;
MENKING, M ;
SOTOS, JF .
JOURNAL OF PEDIATRICS, 1968, 72 (01) :81-+
[14]   HYPOGLYCEMIA IN HYPOPITUITARY CHILDREN [J].
HOPWOOD, NJ ;
FORSMAN, PJ ;
KENNY, FM ;
DRASH, AL .
AMERICAN JOURNAL OF DISEASES OF CHILDREN, 1975, 129 (08) :918-926
[15]  
HOYT WF, 1970, LANCET, V1, P893
[16]   HYPOPLASIA OF ANTERIOR-PITUITARY AND NEONATAL HYPOGLYCEMIA [J].
JOHNSON, JD ;
HANSEN, RC ;
ALBRITTON, WL ;
WERTHEMANN, U ;
CHRISTIANSEN, RO .
JOURNAL OF PEDIATRICS, 1973, 82 (04) :634-641
[17]   NEONATAL THYROID-FUNCTION IN CONGENITAL HYPOTHYROIDISM [J].
KLEIN, AH ;
FOLEY, TP ;
LARSEN, PR ;
AGUSTIN, AV ;
HOPWOOD, NJ .
JOURNAL OF PEDIATRICS, 1976, 89 (04) :545-549
[18]   CONGENITAL HYPOPITUITARISM ASSOCIATED WITH NEONATAL HYPOGLYCEMIA AND MICROPHALLUS - 4 CASES SECONDARY TO HYPOTHALAMIC HORMONE DEFICIENCIES [J].
LOVINGER, RD ;
KAPLAN, SL ;
GRUMBACH, MM .
JOURNAL OF PEDIATRICS, 1975, 87 (06) :1171-1181
[19]   HYPERGLUCAGONISM INDUCED BY GLUCOCORTICOID TREATMENT IN MAN [J].
MARCO, J ;
CALLE, C ;
ROMAN, D ;
DIAZFIER.M ;
VILLANUEVA, ML ;
VALVERDE, I .
NEW ENGLAND JOURNAL OF MEDICINE, 1973, 288 (03) :128-131
[20]   GLUCOSE AND LIPID HOMEOSTASIS IN ABSENCE OF HUMAN GROWTH HORMONE [J].
MERIMEE, TJ ;
FELIG, P ;
MARLISS, E ;
FINEBERG, SE ;
CAHILL, GG .
JOURNAL OF CLINICAL INVESTIGATION, 1971, 50 (03) :574-&