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EVIDENCE AGAINST ALPHA-HYDROXYPHYTANIC ACID AS AN INTERMEDIATE IN THE METABOLISM OF PHYTANIC ACID
被引:29
作者
:
SKJELDAL, OH
论文数:
0
引用数:
0
h-index:
0
SKJELDAL, OH
STOKKE, O
论文数:
0
引用数:
0
h-index:
0
STOKKE, O
机构
:
来源
:
SCANDINAVIAN JOURNAL OF CLINICAL & LABORATORY INVESTIGATION
|
1988年
/ 48卷
/ 01期
关键词
:
D O I
:
10.3109/00365518809086619
中图分类号
:
R-3 [医学研究方法];
R3 [基础医学];
学科分类号
:
1001 ;
摘要
:
引用
收藏
页码:97 / 102
页数:6
相关论文
共 15 条
[1]
SUCCINIC DEHYDROGENASE
[J].
BONNER, WD
论文数:
0
引用数:
0
h-index:
0
BONNER, WD
.
METHODS IN ENZYMOLOGY,
1955,
1
:722
-729
[2]
ASSAY OF CATALASES AND PEROXIDASES
[J].
CHANCE, B
论文数:
0
引用数:
0
h-index:
0
CHANCE, B
;
MAEHLY, AC
论文数:
0
引用数:
0
h-index:
0
MAEHLY, AC
.
METHODS IN ENZYMOLOGY,
1955,
2
:764
-775
[3]
REFSUMS DISEASE - CHARACTERIZATION OF ENZYME DEFECT IN CELL CULTURE
[J].
HERNDON, JH
论文数:
0
引用数:
0
h-index:
0
HERNDON, JH
;
STEINBER.D
论文数:
0
引用数:
0
h-index:
0
STEINBER.D
;
UHLENDOR.BW
论文数:
0
引用数:
0
h-index:
0
UHLENDOR.BW
;
FALES, HM
论文数:
0
引用数:
0
h-index:
0
FALES, HM
.
JOURNAL OF CLINICAL INVESTIGATION,
1969,
48
(06)
:1017
-&
[4]
A MAJOR PATHWAY FOR MAMMALIAN OXIDATIVE DEGRADATION OF PHYTANIC ACID
[J].
MIZE, CE
论文数:
0
引用数:
0
h-index:
0
机构:
Molecular Disease Branch, National Heart Institute, National Institutes of Health, Bethesda
MIZE, CE
;
AVIGAN, J
论文数:
0
引用数:
0
h-index:
0
机构:
Molecular Disease Branch, National Heart Institute, National Institutes of Health, Bethesda
AVIGAN, J
;
STEINBER.D
论文数:
0
引用数:
0
h-index:
0
机构:
Molecular Disease Branch, National Heart Institute, National Institutes of Health, Bethesda
STEINBER.D
;
PITTMAN, RC
论文数:
0
引用数:
0
h-index:
0
机构:
Molecular Disease Branch, National Heart Institute, National Institutes of Health, Bethesda
PITTMAN, RC
;
FALES, HM
论文数:
0
引用数:
0
h-index:
0
机构:
Molecular Disease Branch, National Heart Institute, National Institutes of Health, Bethesda
FALES, HM
;
MILNE, GWA
论文数:
0
引用数:
0
h-index:
0
机构:
Molecular Disease Branch, National Heart Institute, National Institutes of Health, Bethesda
MILNE, GWA
.
BIOCHIMICA ET BIOPHYSICA ACTA,
1969,
176
(04)
:720
-&
[5]
PATTERNS OF REFSUMS DISEASE - PHYTANIC ACID OXIDASE DEFICIENCY
[J].
POULOS, A
论文数:
0
引用数:
0
h-index:
0
机构:
PRINCE WALES HOSP,SYDNEY,NSW,AUSTRALIA
POULOS, A
;
POLLARD, AC
论文数:
0
引用数:
0
h-index:
0
机构:
PRINCE WALES HOSP,SYDNEY,NSW,AUSTRALIA
POLLARD, AC
;
MITCHELL, JD
论文数:
0
引用数:
0
h-index:
0
机构:
PRINCE WALES HOSP,SYDNEY,NSW,AUSTRALIA
MITCHELL, JD
;
WISE, G
论文数:
0
引用数:
0
h-index:
0
机构:
PRINCE WALES HOSP,SYDNEY,NSW,AUSTRALIA
WISE, G
;
MORTIMER, G
论文数:
0
引用数:
0
h-index:
0
机构:
PRINCE WALES HOSP,SYDNEY,NSW,AUSTRALIA
MORTIMER, G
.
ARCHIVES OF DISEASE IN CHILDHOOD,
1984,
59
(03)
:222
-229
[6]
INFANTILE PHYTANIC ACID STORAGE DISEASE, A POSSIBLE VARIANT OF REFSUMS DISEASE - 3 CASES, INCLUDING ULTRASTRUCTURAL STUDIES OF THE LIVER
[J].
SCOTTO, JM
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PARIS SUD,HOP ENFANTS,PEDIAT CLIN,F-94270 BICETRE,FRANCE
SCOTTO, JM
;
HADCHOUEL, M
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PARIS SUD,HOP ENFANTS,PEDIAT CLIN,F-94270 BICETRE,FRANCE
HADCHOUEL, M
;
ODIEVRE, M
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PARIS SUD,HOP ENFANTS,PEDIAT CLIN,F-94270 BICETRE,FRANCE
ODIEVRE, M
;
LAUDAT, MH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PARIS SUD,HOP ENFANTS,PEDIAT CLIN,F-94270 BICETRE,FRANCE
LAUDAT, MH
;
SAUDUBRAY, JM
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PARIS SUD,HOP ENFANTS,PEDIAT CLIN,F-94270 BICETRE,FRANCE
SAUDUBRAY, JM
;
DULAC, O
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PARIS SUD,HOP ENFANTS,PEDIAT CLIN,F-94270 BICETRE,FRANCE
DULAC, O
;
BEUCLER, I
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PARIS SUD,HOP ENFANTS,PEDIAT CLIN,F-94270 BICETRE,FRANCE
BEUCLER, I
;
论文数:
引用数:
h-index:
机构:
BEAUNE, P
.
JOURNAL OF INHERITED METABOLIC DISEASE,
1982,
5
(02)
:83
-90
[7]
PHYTANIC ACID OXIDASE ACTIVITY IN CULTURED SKIN FIBROBLASTS - DIAGNOSTIC USEFULNESS AND LIMITATIONS
[J].
SKJELDAL, OH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV OSLO,RIKSHOSP,PAEDIAT RES INST,N-0027 OSLO 1,NORWAY
UNIV OSLO,RIKSHOSP,PAEDIAT RES INST,N-0027 OSLO 1,NORWAY
SKJELDAL, OH
;
STOKKE, O
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV OSLO,RIKSHOSP,PAEDIAT RES INST,N-0027 OSLO 1,NORWAY
UNIV OSLO,RIKSHOSP,PAEDIAT RES INST,N-0027 OSLO 1,NORWAY
STOKKE, O
;
NORSETH, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV OSLO,RIKSHOSP,PAEDIAT RES INST,N-0027 OSLO 1,NORWAY
UNIV OSLO,RIKSHOSP,PAEDIAT RES INST,N-0027 OSLO 1,NORWAY
NORSETH, J
;
LIE, SO
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV OSLO,RIKSHOSP,PAEDIAT RES INST,N-0027 OSLO 1,NORWAY
UNIV OSLO,RIKSHOSP,PAEDIAT RES INST,N-0027 OSLO 1,NORWAY
LIE, SO
.
SCANDINAVIAN JOURNAL OF CLINICAL & LABORATORY INVESTIGATION,
1986,
46
(03)
:283
-287
[8]
CLINICAL AND BIOCHEMICAL HETEROGENEITY IN CONDITIONS WITH PHYTANIC ACID ACCUMULATION
[J].
SKJELDAL, OH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV OSLO,RIKSHOSP,INST CLIN BIOCHEM,OSLO,NORWAY
SKJELDAL, OH
;
STOKKE, O
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV OSLO,RIKSHOSP,INST CLIN BIOCHEM,OSLO,NORWAY
STOKKE, O
;
REFSUM, S
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV OSLO,RIKSHOSP,INST CLIN BIOCHEM,OSLO,NORWAY
REFSUM, S
;
NORSETH, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV OSLO,RIKSHOSP,INST CLIN BIOCHEM,OSLO,NORWAY
NORSETH, J
;
PETIT, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV OSLO,RIKSHOSP,INST CLIN BIOCHEM,OSLO,NORWAY
PETIT, H
.
JOURNAL OF THE NEUROLOGICAL SCIENCES,
1987,
77
(01)
:87
-96
[9]
THE SUBCELLULAR-LOCALIZATION OF PHYTANIC ACID OXIDASE IN RAT-LIVER
[J].
SKJELDAL, OH
论文数:
0
引用数:
0
h-index:
0
SKJELDAL, OH
;
STOKKE, O
论文数:
0
引用数:
0
h-index:
0
STOKKE, O
.
BIOCHIMICA ET BIOPHYSICA ACTA,
1987,
921
(01)
:38
-42
[10]
Steinberg D., 1983, METABOLIC BASIS INHE, P731
←
1
2
→
共 15 条
[1]
SUCCINIC DEHYDROGENASE
[J].
BONNER, WD
论文数:
0
引用数:
0
h-index:
0
BONNER, WD
.
METHODS IN ENZYMOLOGY,
1955,
1
:722
-729
[2]
ASSAY OF CATALASES AND PEROXIDASES
[J].
CHANCE, B
论文数:
0
引用数:
0
h-index:
0
CHANCE, B
;
MAEHLY, AC
论文数:
0
引用数:
0
h-index:
0
MAEHLY, AC
.
METHODS IN ENZYMOLOGY,
1955,
2
:764
-775
[3]
REFSUMS DISEASE - CHARACTERIZATION OF ENZYME DEFECT IN CELL CULTURE
[J].
HERNDON, JH
论文数:
0
引用数:
0
h-index:
0
HERNDON, JH
;
STEINBER.D
论文数:
0
引用数:
0
h-index:
0
STEINBER.D
;
UHLENDOR.BW
论文数:
0
引用数:
0
h-index:
0
UHLENDOR.BW
;
FALES, HM
论文数:
0
引用数:
0
h-index:
0
FALES, HM
.
JOURNAL OF CLINICAL INVESTIGATION,
1969,
48
(06)
:1017
-&
[4]
A MAJOR PATHWAY FOR MAMMALIAN OXIDATIVE DEGRADATION OF PHYTANIC ACID
[J].
MIZE, CE
论文数:
0
引用数:
0
h-index:
0
机构:
Molecular Disease Branch, National Heart Institute, National Institutes of Health, Bethesda
MIZE, CE
;
AVIGAN, J
论文数:
0
引用数:
0
h-index:
0
机构:
Molecular Disease Branch, National Heart Institute, National Institutes of Health, Bethesda
AVIGAN, J
;
STEINBER.D
论文数:
0
引用数:
0
h-index:
0
机构:
Molecular Disease Branch, National Heart Institute, National Institutes of Health, Bethesda
STEINBER.D
;
PITTMAN, RC
论文数:
0
引用数:
0
h-index:
0
机构:
Molecular Disease Branch, National Heart Institute, National Institutes of Health, Bethesda
PITTMAN, RC
;
FALES, HM
论文数:
0
引用数:
0
h-index:
0
机构:
Molecular Disease Branch, National Heart Institute, National Institutes of Health, Bethesda
FALES, HM
;
MILNE, GWA
论文数:
0
引用数:
0
h-index:
0
机构:
Molecular Disease Branch, National Heart Institute, National Institutes of Health, Bethesda
MILNE, GWA
.
BIOCHIMICA ET BIOPHYSICA ACTA,
1969,
176
(04)
:720
-&
[5]
PATTERNS OF REFSUMS DISEASE - PHYTANIC ACID OXIDASE DEFICIENCY
[J].
POULOS, A
论文数:
0
引用数:
0
h-index:
0
机构:
PRINCE WALES HOSP,SYDNEY,NSW,AUSTRALIA
POULOS, A
;
POLLARD, AC
论文数:
0
引用数:
0
h-index:
0
机构:
PRINCE WALES HOSP,SYDNEY,NSW,AUSTRALIA
POLLARD, AC
;
MITCHELL, JD
论文数:
0
引用数:
0
h-index:
0
机构:
PRINCE WALES HOSP,SYDNEY,NSW,AUSTRALIA
MITCHELL, JD
;
WISE, G
论文数:
0
引用数:
0
h-index:
0
机构:
PRINCE WALES HOSP,SYDNEY,NSW,AUSTRALIA
WISE, G
;
MORTIMER, G
论文数:
0
引用数:
0
h-index:
0
机构:
PRINCE WALES HOSP,SYDNEY,NSW,AUSTRALIA
MORTIMER, G
.
ARCHIVES OF DISEASE IN CHILDHOOD,
1984,
59
(03)
:222
-229
[6]
INFANTILE PHYTANIC ACID STORAGE DISEASE, A POSSIBLE VARIANT OF REFSUMS DISEASE - 3 CASES, INCLUDING ULTRASTRUCTURAL STUDIES OF THE LIVER
[J].
SCOTTO, JM
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PARIS SUD,HOP ENFANTS,PEDIAT CLIN,F-94270 BICETRE,FRANCE
SCOTTO, JM
;
HADCHOUEL, M
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PARIS SUD,HOP ENFANTS,PEDIAT CLIN,F-94270 BICETRE,FRANCE
HADCHOUEL, M
;
ODIEVRE, M
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PARIS SUD,HOP ENFANTS,PEDIAT CLIN,F-94270 BICETRE,FRANCE
ODIEVRE, M
;
LAUDAT, MH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PARIS SUD,HOP ENFANTS,PEDIAT CLIN,F-94270 BICETRE,FRANCE
LAUDAT, MH
;
SAUDUBRAY, JM
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PARIS SUD,HOP ENFANTS,PEDIAT CLIN,F-94270 BICETRE,FRANCE
SAUDUBRAY, JM
;
DULAC, O
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PARIS SUD,HOP ENFANTS,PEDIAT CLIN,F-94270 BICETRE,FRANCE
DULAC, O
;
BEUCLER, I
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV PARIS SUD,HOP ENFANTS,PEDIAT CLIN,F-94270 BICETRE,FRANCE
BEUCLER, I
;
论文数:
引用数:
h-index:
机构:
BEAUNE, P
.
JOURNAL OF INHERITED METABOLIC DISEASE,
1982,
5
(02)
:83
-90
[7]
PHYTANIC ACID OXIDASE ACTIVITY IN CULTURED SKIN FIBROBLASTS - DIAGNOSTIC USEFULNESS AND LIMITATIONS
[J].
SKJELDAL, OH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV OSLO,RIKSHOSP,PAEDIAT RES INST,N-0027 OSLO 1,NORWAY
UNIV OSLO,RIKSHOSP,PAEDIAT RES INST,N-0027 OSLO 1,NORWAY
SKJELDAL, OH
;
STOKKE, O
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV OSLO,RIKSHOSP,PAEDIAT RES INST,N-0027 OSLO 1,NORWAY
UNIV OSLO,RIKSHOSP,PAEDIAT RES INST,N-0027 OSLO 1,NORWAY
STOKKE, O
;
NORSETH, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV OSLO,RIKSHOSP,PAEDIAT RES INST,N-0027 OSLO 1,NORWAY
UNIV OSLO,RIKSHOSP,PAEDIAT RES INST,N-0027 OSLO 1,NORWAY
NORSETH, J
;
LIE, SO
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV OSLO,RIKSHOSP,PAEDIAT RES INST,N-0027 OSLO 1,NORWAY
UNIV OSLO,RIKSHOSP,PAEDIAT RES INST,N-0027 OSLO 1,NORWAY
LIE, SO
.
SCANDINAVIAN JOURNAL OF CLINICAL & LABORATORY INVESTIGATION,
1986,
46
(03)
:283
-287
[8]
CLINICAL AND BIOCHEMICAL HETEROGENEITY IN CONDITIONS WITH PHYTANIC ACID ACCUMULATION
[J].
SKJELDAL, OH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV OSLO,RIKSHOSP,INST CLIN BIOCHEM,OSLO,NORWAY
SKJELDAL, OH
;
STOKKE, O
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV OSLO,RIKSHOSP,INST CLIN BIOCHEM,OSLO,NORWAY
STOKKE, O
;
REFSUM, S
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV OSLO,RIKSHOSP,INST CLIN BIOCHEM,OSLO,NORWAY
REFSUM, S
;
NORSETH, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV OSLO,RIKSHOSP,INST CLIN BIOCHEM,OSLO,NORWAY
NORSETH, J
;
PETIT, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV OSLO,RIKSHOSP,INST CLIN BIOCHEM,OSLO,NORWAY
PETIT, H
.
JOURNAL OF THE NEUROLOGICAL SCIENCES,
1987,
77
(01)
:87
-96
[9]
THE SUBCELLULAR-LOCALIZATION OF PHYTANIC ACID OXIDASE IN RAT-LIVER
[J].
SKJELDAL, OH
论文数:
0
引用数:
0
h-index:
0
SKJELDAL, OH
;
STOKKE, O
论文数:
0
引用数:
0
h-index:
0
STOKKE, O
.
BIOCHIMICA ET BIOPHYSICA ACTA,
1987,
921
(01)
:38
-42
[10]
Steinberg D., 1983, METABOLIC BASIS INHE, P731
←
1
2
→