SPECIFICITY OF GALACTOSYLCERAMIDASE ACTIVATION BY PHOSPHATIDYLSERINE

被引:8
作者
HANADA, E
SUZUKI, K
机构
[1] YESHIVA UNIV ALBERT EINSTEIN COLL MED,SAUL R KOREY DEPT NEUROL,BRONX,NY 10461
[2] YESHIVA UNIV ALBERT EINSTEIN COLL MED,ROSE F KENNEDY CTR RES MENTAL RETARDAT & HUMAN DEV,BRONX,NY 10461
[3] YESHIVA UNIV ALBERT EINSTEIN COLL MED,DEPT NEUROSCI,BRONX,NY 10461
关键词
D O I
10.1016/0005-2760(80)90087-9
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:396 / 402
页数:7
相关论文
共 25 条
[11]   GLOBOID CELL LEUKODYSTROPHY - ADDITIONAL DEFICIENCY OF PSYCHOSINE GALACTOSIDASE [J].
MIYATAKE, T ;
SUZUKI, K .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1972, 48 (03) :538-&
[12]   LOW-MOLECULAR WEIGHT PROTEINS IN SECONDARY LYSOSOMES AS ACTIVATORS OF DIFFERENT SPHINGOLIPID HYDROLASES [J].
MRAZ, W ;
FISCHER, G ;
JATZKEWITZ, H .
FEBS LETTERS, 1976, 67 (01) :104-109
[13]  
NORDEN AGW, 1974, J BIOL CHEM, V249, P7969
[14]  
NORTON WT, 1965, ANN NY ACAD SCI, V122, P77
[15]   LACTOSYLCERAMIDE GALACTOSIDASE - COMPARISON WITH OTHER SPHINGOLIPID HYDROLASES IN DEVELOPING RAT BRAIN [J].
RADIN, NS ;
HOF, L ;
BRADLEY, RM ;
BRADY, RO .
BRAIN RESEARCH, 1969, 14 (02) :497-&
[16]  
SUZUKI Y, 1974, J BIOL CHEM, V249, P2098
[17]   CHEMICAL PATHOLOGY OF KRABBES DISEASE .4. STUDIES OF GALACTOSYLCERAMIDE AND LACTOSYLCERAMIDE BETA-GALACTOSIDASES IN BRAIN, WHITE BLOOD-CELLS AND AMNIOTIC-FLUID CELLS [J].
SVENNERHOLM, L ;
HAKANSSON, G ;
VANIER, MT .
ACTA PAEDIATRICA SCANDINAVICA, 1975, 64 (04) :649-656
[18]  
TANAKA H, 1975, J BIOL CHEM, V250, P2324
[19]   SUBSTRATE SPECIFICITIES OF 2 GENETICALLY DISTINCT HUMAN-BRAIN BETA-GALACTOSIDASES [J].
TANAKA, H ;
SUZUKI, K .
BRAIN RESEARCH, 1977, 122 (02) :325-335
[20]   GLOBOID-CELL LEUKODYSTROPHY (KRABBES DISEASE) - METABOLIC STUDIES WITH CULTURED FIBROBLASTS [J].
TANAKA, H ;
SUZUKI, K .
JOURNAL OF THE NEUROLOGICAL SCIENCES, 1978, 38 (03) :409-419