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GM1-GANGLIOSIDOSIS TYPES-1 AND TYPES-2 - ENZYMATIC DIFFERENCES IN CULTURED FIBROBLASTS
被引:48
作者
:
PINSKY, L
论文数:
0
引用数:
0
h-index:
0
PINSKY, L
POWELL, E
论文数:
0
引用数:
0
h-index:
0
POWELL, E
CALLAHAN, J
论文数:
0
引用数:
0
h-index:
0
CALLAHAN, J
机构
:
来源
:
NATURE
|
1970年
/ 228卷
/ 5276期
关键词
:
D O I
:
10.1038/2281093b0
中图分类号
:
O [数理科学和化学];
P [天文学、地球科学];
Q [生物科学];
N [自然科学总论];
学科分类号
:
07 ;
0710 ;
09 ;
摘要
:
引用
收藏
页码:1093 / &
相关论文
共 12 条
[1]
MAMMALIAN BETA-GALACTOSIDASES
CHYTIL, F
论文数:
0
引用数:
0
h-index:
0
CHYTIL, F
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1965,
19
(05)
: 630
-
&
[2]
DERRY DM, 1968, NEUROLOGY, V18, P34
[3]
AMINO ACID METABOLISM IN MAMMALIAN CELL CULTURES
EAGLE, H
论文数:
0
引用数:
0
h-index:
0
EAGLE, H
[J].
SCIENCE,
1959,
130
(3373)
: 432
-
437
[4]
HURLERS SYNDROME - DEFICIENCY OF A SPECIFIC BETA GALACTOSIDASE ISOENZYME
HO, MW
论文数:
0
引用数:
0
h-index:
0
机构:
Department of Neurosciences, School of Medicine, University of California at San Diego, San Diego
HO, MW
OBRIEN, JS
论文数:
0
引用数:
0
h-index:
0
机构:
Department of Neurosciences, School of Medicine, University of California at San Diego, San Diego
OBRIEN, JS
[J].
SCIENCE,
1969,
165
(3893)
: 611
-
&
[5]
JUNGALWALA FB, 1968, J BIOL CHEM, V243, P4258
[6]
STUDIES ON CELL LINES DEVELOPED FROM TISSUES OF PATIENTS WITH GALACTOSEMIA
KROOTH, RS
论文数:
0
引用数:
0
h-index:
0
KROOTH, RS
WEINBERG, AN
论文数:
0
引用数:
0
h-index:
0
WEINBERG, AN
[J].
JOURNAL OF EXPERIMENTAL MEDICINE,
1961,
113
(06)
: 1155
-
&
[7]
MARTIN GM, 1964, P SOC EXP BIOL MED, V116, P167
[8]
GENERALIZED GANGLIOSIDOSIS
OBRIEN, J
论文数:
0
引用数:
0
h-index:
0
机构:
Division of Neurometabolic Disorders, Department of Neurosciences, School of Medicine, La Jolla, CA
OBRIEN, J
[J].
JOURNAL OF PEDIATRICS,
1969,
75
(02)
: 167
-
&
[9]
ACID HYDROLASES IN SKIN AND PLASMA IN GARGOYLISM DEFICIENCY OF BETA-GALACTOSIDASE IN SKIN
OCKERMAN, PA
论文数:
0
引用数:
0
h-index:
0
机构:
Department of Clinical Chemistry, University of Lund
OCKERMAN, PA
[J].
CLINICA CHIMICA ACTA,
1968,
20
(01)
: 1
-
&
[10]
FRACTIONATION OF 4-METHYLUMBELLIFERYL-BETA-GALACTOSIDASE ACTIVITIES IN LIVER IN GARGOYLISM
OCKERMAN, PA
论文数:
0
引用数:
0
h-index:
0
OCKERMAN, PA
HULTBERG, B
论文数:
0
引用数:
0
h-index:
0
HULTBERG, B
[J].
SCANDINAVIAN JOURNAL OF CLINICAL & LABORATORY INVESTIGATION,
1968,
22
(03)
: 199
-
&
←
1
2
→
共 12 条
[1]
MAMMALIAN BETA-GALACTOSIDASES
CHYTIL, F
论文数:
0
引用数:
0
h-index:
0
CHYTIL, F
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1965,
19
(05)
: 630
-
&
[2]
DERRY DM, 1968, NEUROLOGY, V18, P34
[3]
AMINO ACID METABOLISM IN MAMMALIAN CELL CULTURES
EAGLE, H
论文数:
0
引用数:
0
h-index:
0
EAGLE, H
[J].
SCIENCE,
1959,
130
(3373)
: 432
-
437
[4]
HURLERS SYNDROME - DEFICIENCY OF A SPECIFIC BETA GALACTOSIDASE ISOENZYME
HO, MW
论文数:
0
引用数:
0
h-index:
0
机构:
Department of Neurosciences, School of Medicine, University of California at San Diego, San Diego
HO, MW
OBRIEN, JS
论文数:
0
引用数:
0
h-index:
0
机构:
Department of Neurosciences, School of Medicine, University of California at San Diego, San Diego
OBRIEN, JS
[J].
SCIENCE,
1969,
165
(3893)
: 611
-
&
[5]
JUNGALWALA FB, 1968, J BIOL CHEM, V243, P4258
[6]
STUDIES ON CELL LINES DEVELOPED FROM TISSUES OF PATIENTS WITH GALACTOSEMIA
KROOTH, RS
论文数:
0
引用数:
0
h-index:
0
KROOTH, RS
WEINBERG, AN
论文数:
0
引用数:
0
h-index:
0
WEINBERG, AN
[J].
JOURNAL OF EXPERIMENTAL MEDICINE,
1961,
113
(06)
: 1155
-
&
[7]
MARTIN GM, 1964, P SOC EXP BIOL MED, V116, P167
[8]
GENERALIZED GANGLIOSIDOSIS
OBRIEN, J
论文数:
0
引用数:
0
h-index:
0
机构:
Division of Neurometabolic Disorders, Department of Neurosciences, School of Medicine, La Jolla, CA
OBRIEN, J
[J].
JOURNAL OF PEDIATRICS,
1969,
75
(02)
: 167
-
&
[9]
ACID HYDROLASES IN SKIN AND PLASMA IN GARGOYLISM DEFICIENCY OF BETA-GALACTOSIDASE IN SKIN
OCKERMAN, PA
论文数:
0
引用数:
0
h-index:
0
机构:
Department of Clinical Chemistry, University of Lund
OCKERMAN, PA
[J].
CLINICA CHIMICA ACTA,
1968,
20
(01)
: 1
-
&
[10]
FRACTIONATION OF 4-METHYLUMBELLIFERYL-BETA-GALACTOSIDASE ACTIVITIES IN LIVER IN GARGOYLISM
OCKERMAN, PA
论文数:
0
引用数:
0
h-index:
0
OCKERMAN, PA
HULTBERG, B
论文数:
0
引用数:
0
h-index:
0
HULTBERG, B
[J].
SCANDINAVIAN JOURNAL OF CLINICAL & LABORATORY INVESTIGATION,
1968,
22
(03)
: 199
-
&
←
1
2
→