AFFINITY-CHROMATOGRAPHY OF LYSOSOMAL-ENZYMES IN PLASMA, URINE AND FIBROBLASTS OF PATIENTS WITH MUCOLIPIDOSIS ML-II AND ML-III

被引：6

作者：

DENTANDT, WR

机构：

来源：

CLINICA CHIMICA ACTA | 1980年 / 102卷 / 2-3期

关键词：

D O I：

10.1016/0009-8981(80)90033-9

中图分类号：

R446 [实验室诊断]; R-33 [实验医学、医学实验];

学科分类号：

1001 ;

摘要：

引用

页码：199 / 205

页数：7

共 28 条

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[5]

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[6] I-CELL DISEASE (MUCOLIPIDOSIS II) - RESOLUTION OF N-ACETYL-BETA-D-GLUCOSAMINIDASE AND ALPHA-L-FUCOSIDASE COMPONENTS BY DEAE-CELLULOSE CHROMATOGRAPHY [J].

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[7] PROTEIN-CARBOHYDRATE INTERACTION .2. INHIBITION STUDIES ON INTERACTION OF CONCANAVALIN A WITH POLYSACCHARIDES [J].

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SMITH, EE .

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[8] PROTEIN-CARBOHYDRATE INTERACTION .I. INTERACTION OF POLYSACCHARIDES WITH CONCANAVALIN A [J].

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MERRICK, JM .

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[9] HYPOTHESIS FOR I-CELL DISEASE - DEFECTIVE HYDROLASES THAT DO NOT ENTER LYSOSOMES [J].

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[10]

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