Primary cardiac gastrinoma causing Zollinger-Ellison syndrome

被引:26
作者
Gibril, F
Curtis, LT
Termanini, B
Fritsch, MK
Lubensky, IA
Doppman, JL
Jensen, RT
机构
[1] NIDDK, DDB, NIH, BETHESDA, MD 20892 USA
[2] NCI, PATHOL LAB, NIH, BETHESDA, MD 20892 USA
[3] NIH, WARREN GRANT MAGNUSON CLIN CTR, DEPT DIAGNOST RADIOL, BETHESDA, MD 20892 USA
[4] TETON VALLEY MED CTR, DRIGGS, ID USA
关键词
D O I
10.1053/gast.1997.v112.pm9024311
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
Primary cardiac tumors are rare, and there are no reports of patients with a functional gastroenteropancreatic tumor syndrome caused by such a tumor, This case report describes a patient with a cardiac gastrinoma causing Zollinger-Ellison syndrome. Evidence is presented that this tumor represents a primary cardiac tumor. The exact identification of this gastrinoma in an extra-abdominal site was facilitated by the use of [In-111-DTPA-DPhe(1)]octreotide scanning for somatostatin receptors, which these tumors characteristically possess in high numbers, The recent availability of this novel localization method may facilitate identification of extra-abdominal sites in an increasing proportion of patients with gastrinomas and related neuroendocrine functional tumors in which no intra-abdominal primary tumor is currently found.
引用
收藏
页码:567 / 574
页数:8
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