Persistent pulmonary hypertension of newborn due to congenital capillary alveolar dysplasia

被引:22
作者
Singh, SA
Ibrahim, T
Clark, DJ
Taylor, RS
George, DH
机构
[1] Univ Calgary, Foothills Med Ctr, Dept Pathol, Calgary, AB T2N 2T9, Canada
[2] Univ Calgary, Foothills Med Ctr, Dept Neonatol, Calgary, AB T2N 2T9, Canada
关键词
alveolar capillary dysplasia; persistent pulmonary hypertension; neonate;
D O I
10.1002/ppul.20244
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Congenital alveolar capillary dysplasia is a rare and fatal cause of pulmonary hypertension in neonates. We report on a term baby with severe pulmonary hypertension unresponsive to high-frequency ventilation and nitric oxide. A diagnosis of alveolar capillary dysplasia was established on autopsy We review the literature regarding pathophysiology, clinical presentations, associated malformations, and treatment trials.
引用
收藏
页码:349 / 353
页数:5
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