Mechanisms of disease - Folding of secretory and membrane proteins

[51] Mechanisms of disease - Mechanisms of muscle wasting - The role of the ubiquitin-proteasome pathway [J]. NEW ENGLAND JOURNAL OF MEDICINE, 1996, 335 (25) : 1897 - 1905

[52] NIGAM SK, 1994, J BIOL CHEM, V269, P1744

[53] OCKNER RK, 1993, PROGR LIVER DIS, V11, P139

[54] Oksche A, 1996, MOL PHARMACOL, V50, P820

[55] MUTANT (DELTA-F508) CYSTIC-FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR CL- CHANNEL IS FUNCTIONAL WHEN RETAINED IN ENDOPLASMIC-RETICULUM OF MAMMALIAN-CELLS [J]. JOURNAL OF BIOLOGICAL CHEMISTRY, 1995, 270 (21) : 12347 - 12350

[56] PIND S, 1994, J BIOL CHEM, V269, P12784

[57] Degradation of a mutant secretory protein, alpha(1)-antitrypsin Z, in the endoplasmic reticulum requires proteasome activity [J]. JOURNAL OF BIOLOGICAL CHEMISTRY, 1996, 271 (37) : 22791 - 22795

[58] Fibrillin mutations in Marfan syndrome and related phenotypes [J]. CURRENT OPINION IN GENETICS & DEVELOPMENT, 1996, 6 (03) : 309 - 315

[59] THE MOLECULAR-BIOLOGY OF CYSTIC-FIBROSIS [J]. ANNUAL REVIEW OF MEDICINE, 1993, 44 : 133 - 144

[60] Shamu Caroline E., 1994, Trends in Cell Biology, V4, P56, DOI 10.1016/0962-8924(94)90011-6

[51] Mechanisms of disease - Mechanisms of muscle wasting - The role of the ubiquitin-proteasome pathway [J]. NEW ENGLAND JOURNAL OF MEDICINE, 1996, 335 (25) : 1897 - 1905

[52] NIGAM SK, 1994, J BIOL CHEM, V269, P1744

[53] OCKNER RK, 1993, PROGR LIVER DIS, V11, P139

[54] Oksche A, 1996, MOL PHARMACOL, V50, P820

[55] MUTANT (DELTA-F508) CYSTIC-FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR CL- CHANNEL IS FUNCTIONAL WHEN RETAINED IN ENDOPLASMIC-RETICULUM OF MAMMALIAN-CELLS [J]. JOURNAL OF BIOLOGICAL CHEMISTRY, 1995, 270 (21) : 12347 - 12350

[56] PIND S, 1994, J BIOL CHEM, V269, P12784

[57] Degradation of a mutant secretory protein, alpha(1)-antitrypsin Z, in the endoplasmic reticulum requires proteasome activity [J]. JOURNAL OF BIOLOGICAL CHEMISTRY, 1996, 271 (37) : 22791 - 22795

[58] Fibrillin mutations in Marfan syndrome and related phenotypes [J]. CURRENT OPINION IN GENETICS & DEVELOPMENT, 1996, 6 (03) : 309 - 315

[59] THE MOLECULAR-BIOLOGY OF CYSTIC-FIBROSIS [J]. ANNUAL REVIEW OF MEDICINE, 1993, 44 : 133 - 144

[60] Shamu Caroline E., 1994, Trends in Cell Biology, V4, P56, DOI 10.1016/0962-8924(94)90011-6