PEROXISOMAL VERY LONG-CHAIN FATTY-ACID BETA-OXIDATION IN HUMAN-SKIN FIBROBLASTS - ACTIVITY IN ZELLWEGER SYNDROME AND OTHER PEROXISOMAL DISORDERS

被引:39
作者
WANDERS, RJA
VANROERMUND, CWT
VANWIJLAND, MJA
HEIKOOP, J
SCHUTGENS, RBH
SCHRAM, AW
TAGER, JM
VANDENBOSCH, H
POLLTHE, BT
SAUDUBRAY, JM
MOSER, HW
MOSER, AB
机构
[1] UNIV AMSTERDAM,BIOCHEM LAB,AMSTERDAM,NETHERLANDS
[2] STATE UNIV UTRECHT,BIOCHEM LAB,UTRECHT,NETHERLANDS
[3] HOP ENFANTS MALAD,PARIS,FRANCE
[4] JOHN F KENNEDY INST,BALTIMORE,MD 21205
关键词
D O I
10.1016/0009-8981(87)90428-1
中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
摘要
引用
收藏
页码:255 / 263
页数:9
相关论文
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