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DEFICIENCY OF PLASMALOGENS IN THE CEREBRO-HEPATO-RENAL (ZELLWEGER) SYNDROME
被引:78
作者
:
HEYMANS, HSA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HOSP AMSTERDAM,DEPT PEDIAT,1105 AZ AMSTERDAM,NETHERLANDS
HEYMANS, HSA
VANDERBOSCH, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HOSP AMSTERDAM,DEPT PEDIAT,1105 AZ AMSTERDAM,NETHERLANDS
VANDERBOSCH, H
SCHUTGENS, RBH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HOSP AMSTERDAM,DEPT PEDIAT,1105 AZ AMSTERDAM,NETHERLANDS
SCHUTGENS, RBH
TEGELAERS, WHH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HOSP AMSTERDAM,DEPT PEDIAT,1105 AZ AMSTERDAM,NETHERLANDS
TEGELAERS, WHH
WALTHER, JU
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HOSP AMSTERDAM,DEPT PEDIAT,1105 AZ AMSTERDAM,NETHERLANDS
WALTHER, JU
MULLERHOCKER, J
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HOSP AMSTERDAM,DEPT PEDIAT,1105 AZ AMSTERDAM,NETHERLANDS
MULLERHOCKER, J
BORST, P
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV HOSP AMSTERDAM,DEPT PEDIAT,1105 AZ AMSTERDAM,NETHERLANDS
BORST, P
机构
:
[1]
UNIV HOSP AMSTERDAM,DEPT PEDIAT,1105 AZ AMSTERDAM,NETHERLANDS
[2]
STATE UNIV UTRECHT,BIOCHEM LAB,UTRECHT,NETHERLANDS
[3]
UNIV MUNICH,KINDER POLIKLIN,D-8000 MUNICH 2,FED REP GER
[4]
UNIV MUNICH,INST PATHOL,D-8000 MUNICH 2,FED REP GER
[5]
UNIV AMSTERDAM,BIOCHEM LAB,AMSTERDAM,NETHERLANDS
来源
:
EUROPEAN JOURNAL OF PEDIATRICS
|
1984年
/ 142卷
/ 01期
关键词
:
D O I
:
10.1007/BF00442582
中图分类号
:
R72 [儿科学];
学科分类号
:
100202 ;
摘要
:
引用
收藏
页码:10 / 15
页数:6
相关论文
共 27 条
[21]
STUDIES ON MICROPEROXISOMES .5. ARE MICROPEROXISOMES UBIQUITOUS IN MAMMALIAN-CELLS
NOVIKOFF, AB
论文数:
0
引用数:
0
h-index:
0
机构:
YESHIVA UNIV, ALBERT EINSTEIN COLL MED, DEPT PATHOL, BRONX, NY 10461 USA
YESHIVA UNIV, ALBERT EINSTEIN COLL MED, DEPT PATHOL, BRONX, NY 10461 USA
NOVIKOFF, AB
NOVIKOFF, PM
论文数:
0
引用数:
0
h-index:
0
机构:
YESHIVA UNIV, ALBERT EINSTEIN COLL MED, DEPT PATHOL, BRONX, NY 10461 USA
YESHIVA UNIV, ALBERT EINSTEIN COLL MED, DEPT PATHOL, BRONX, NY 10461 USA
NOVIKOFF, PM
DAVIS, C
论文数:
0
引用数:
0
h-index:
0
机构:
YESHIVA UNIV, ALBERT EINSTEIN COLL MED, DEPT PATHOL, BRONX, NY 10461 USA
YESHIVA UNIV, ALBERT EINSTEIN COLL MED, DEPT PATHOL, BRONX, NY 10461 USA
DAVIS, C
QUINTANA, N
论文数:
0
引用数:
0
h-index:
0
机构:
YESHIVA UNIV, ALBERT EINSTEIN COLL MED, DEPT PATHOL, BRONX, NY 10461 USA
YESHIVA UNIV, ALBERT EINSTEIN COLL MED, DEPT PATHOL, BRONX, NY 10461 USA
QUINTANA, N
[J].
JOURNAL OF HISTOCHEMISTRY & CYTOCHEMISTRY,
1973,
21
(08)
: 737
-
755
[22]
OBRIEN JS, 1965, J LIPID RES, V6, P537
[23]
2 DIMENSIONAL THIN LAYER CHROMATOGRAPHIC SEPARATION OF POLAR LIPIDS AND DETERMINATION OF PHOSPHOLIPIDS BY PHOSPHORUS ANALYSIS OF SPOTS
ROUSER, G
论文数:
0
引用数:
0
h-index:
0
ROUSER, G
FLEISCHER, S
论文数:
0
引用数:
0
h-index:
0
FLEISCHER, S
YAMAMOTO, A
论文数:
0
引用数:
0
h-index:
0
YAMAMOTO, A
[J].
LIPIDS,
1970,
5
(05)
: 494
-
+
[24]
FATTY-ACID COMPOSITION OF VARIOUS LIPID FRACTIONS ISOLATED FROM ERYTHROCYTES AND BLOOD-PLASMA OF PATIENTS WITH DUCHENNE AND CONGENITAL MYOTONIC MUSCULAR-DYSTROPHY
RUITENBEEK, W
论文数:
0
引用数:
0
h-index:
0
RUITENBEEK, W
[J].
CLINICA CHIMICA ACTA,
1978,
89
(01)
: 99
-
110
[25]
METABOLIC PATHWAYS IN PEROXISOMES AND GLYOXYSOMES
TOLBERT, NE
论文数:
0
引用数:
0
h-index:
0
TOLBERT, NE
[J].
ANNUAL REVIEW OF BIOCHEMISTRY,
1981,
50
: 133
-
157
[26]
BIOCHEMICAL-STUDIES IN THE LIVER AND MUSCLE OF PATIENTS WITH ZELLWEGER SYNDROME
TRIJBELS, JMF
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
TRIJBELS, JMF
BERDEN, JA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
BERDEN, JA
MONNENS, LAH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
MONNENS, LAH
WILLEMS, JL
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
WILLEMS, JL
JANSSEN, AJM
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
JANSSEN, AJM
SCHUTGENS, RBH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
SCHUTGENS, RBH
VANDENBROEKVANESSEN, M
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
VANDENBROEKVANESSEN, M
[J].
PEDIATRIC RESEARCH,
1983,
17
(06)
: 514
-
517
[27]
METABOLIC DISORDER SIMILAR TO ZELLWEGER SYNDROME WITH HEPATIC ACATALASIA AND ABSENCE OF PEROXISOMES, ALTERED CONTENT AND REDOX STATE OF CYTOCHROMES, AND INFANTILE CIRRHOSIS WITH HEMOSIDEROSIS
VERSMOLD, HT
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
VERSMOLD, HT
BREMER, HI
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
BREMER, HI
HERZOG, V
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
HERZOG, V
SIEGEL, G
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
SIEGEL, G
BASSEWITZ, DBV
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
BASSEWITZ, DBV
IRLE, U
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
IRLE, U
VOSS, HV
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
VOSS, HV
LOMBECK, I
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
LOMBECK, I
BRAUSER, B
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
BRAUSER, B
[J].
EUROPEAN JOURNAL OF PEDIATRICS,
1977,
124
(04)
: 261
-
275
←
1
2
3
→
共 27 条
[21]
STUDIES ON MICROPEROXISOMES .5. ARE MICROPEROXISOMES UBIQUITOUS IN MAMMALIAN-CELLS
NOVIKOFF, AB
论文数:
0
引用数:
0
h-index:
0
机构:
YESHIVA UNIV, ALBERT EINSTEIN COLL MED, DEPT PATHOL, BRONX, NY 10461 USA
YESHIVA UNIV, ALBERT EINSTEIN COLL MED, DEPT PATHOL, BRONX, NY 10461 USA
NOVIKOFF, AB
NOVIKOFF, PM
论文数:
0
引用数:
0
h-index:
0
机构:
YESHIVA UNIV, ALBERT EINSTEIN COLL MED, DEPT PATHOL, BRONX, NY 10461 USA
YESHIVA UNIV, ALBERT EINSTEIN COLL MED, DEPT PATHOL, BRONX, NY 10461 USA
NOVIKOFF, PM
DAVIS, C
论文数:
0
引用数:
0
h-index:
0
机构:
YESHIVA UNIV, ALBERT EINSTEIN COLL MED, DEPT PATHOL, BRONX, NY 10461 USA
YESHIVA UNIV, ALBERT EINSTEIN COLL MED, DEPT PATHOL, BRONX, NY 10461 USA
DAVIS, C
QUINTANA, N
论文数:
0
引用数:
0
h-index:
0
机构:
YESHIVA UNIV, ALBERT EINSTEIN COLL MED, DEPT PATHOL, BRONX, NY 10461 USA
YESHIVA UNIV, ALBERT EINSTEIN COLL MED, DEPT PATHOL, BRONX, NY 10461 USA
QUINTANA, N
[J].
JOURNAL OF HISTOCHEMISTRY & CYTOCHEMISTRY,
1973,
21
(08)
: 737
-
755
[22]
OBRIEN JS, 1965, J LIPID RES, V6, P537
[23]
2 DIMENSIONAL THIN LAYER CHROMATOGRAPHIC SEPARATION OF POLAR LIPIDS AND DETERMINATION OF PHOSPHOLIPIDS BY PHOSPHORUS ANALYSIS OF SPOTS
ROUSER, G
论文数:
0
引用数:
0
h-index:
0
ROUSER, G
FLEISCHER, S
论文数:
0
引用数:
0
h-index:
0
FLEISCHER, S
YAMAMOTO, A
论文数:
0
引用数:
0
h-index:
0
YAMAMOTO, A
[J].
LIPIDS,
1970,
5
(05)
: 494
-
+
[24]
FATTY-ACID COMPOSITION OF VARIOUS LIPID FRACTIONS ISOLATED FROM ERYTHROCYTES AND BLOOD-PLASMA OF PATIENTS WITH DUCHENNE AND CONGENITAL MYOTONIC MUSCULAR-DYSTROPHY
RUITENBEEK, W
论文数:
0
引用数:
0
h-index:
0
RUITENBEEK, W
[J].
CLINICA CHIMICA ACTA,
1978,
89
(01)
: 99
-
110
[25]
METABOLIC PATHWAYS IN PEROXISOMES AND GLYOXYSOMES
TOLBERT, NE
论文数:
0
引用数:
0
h-index:
0
TOLBERT, NE
[J].
ANNUAL REVIEW OF BIOCHEMISTRY,
1981,
50
: 133
-
157
[26]
BIOCHEMICAL-STUDIES IN THE LIVER AND MUSCLE OF PATIENTS WITH ZELLWEGER SYNDROME
TRIJBELS, JMF
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
TRIJBELS, JMF
BERDEN, JA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
BERDEN, JA
MONNENS, LAH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
MONNENS, LAH
WILLEMS, JL
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
WILLEMS, JL
JANSSEN, AJM
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
JANSSEN, AJM
SCHUTGENS, RBH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
SCHUTGENS, RBH
VANDENBROEKVANESSEN, M
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
VANDENBROEKVANESSEN, M
[J].
PEDIATRIC RESEARCH,
1983,
17
(06)
: 514
-
517
[27]
METABOLIC DISORDER SIMILAR TO ZELLWEGER SYNDROME WITH HEPATIC ACATALASIA AND ABSENCE OF PEROXISOMES, ALTERED CONTENT AND REDOX STATE OF CYTOCHROMES, AND INFANTILE CIRRHOSIS WITH HEMOSIDEROSIS
VERSMOLD, HT
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
VERSMOLD, HT
BREMER, HI
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
BREMER, HI
HERZOG, V
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
HERZOG, V
SIEGEL, G
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
SIEGEL, G
BASSEWITZ, DBV
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
BASSEWITZ, DBV
IRLE, U
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
IRLE, U
VOSS, HV
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
VOSS, HV
LOMBECK, I
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
LOMBECK, I
BRAUSER, B
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
BRAUSER, B
[J].
EUROPEAN JOURNAL OF PEDIATRICS,
1977,
124
(04)
: 261
-
275
←
1
2
3
→