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SEVERE PLASMALOGEN DEFICIENCY IN TISSUES OF INFANTS WITHOUT PEROXISOMES (ZELLWEGER SYNDROME)
被引:281
作者
:
HEYMANS, HSA
论文数:
0
引用数:
0
h-index:
0
机构:
STATE UNIV UTRECHT,BIOCHEM LAB,UTRECHT,NETHERLANDS
HEYMANS, HSA
SCHUTGENS, RBH
论文数:
0
引用数:
0
h-index:
0
机构:
STATE UNIV UTRECHT,BIOCHEM LAB,UTRECHT,NETHERLANDS
SCHUTGENS, RBH
TAN, R
论文数:
0
引用数:
0
h-index:
0
机构:
STATE UNIV UTRECHT,BIOCHEM LAB,UTRECHT,NETHERLANDS
TAN, R
VANDENBOSCH, H
论文数:
0
引用数:
0
h-index:
0
机构:
STATE UNIV UTRECHT,BIOCHEM LAB,UTRECHT,NETHERLANDS
VANDENBOSCH, H
BORST, P
论文数:
0
引用数:
0
h-index:
0
机构:
STATE UNIV UTRECHT,BIOCHEM LAB,UTRECHT,NETHERLANDS
BORST, P
机构
:
[1]
STATE UNIV UTRECHT,BIOCHEM LAB,UTRECHT,NETHERLANDS
[2]
UNIV AMSTERDAM,BIOCHEM LAB,AMSTERDAM,NETHERLANDS
来源
:
NATURE
|
1983年
/ 306卷
/ 5938期
关键词
:
D O I
:
10.1038/306069a0
中图分类号
:
O [数理科学和化学];
P [天文学、地球科学];
Q [生物科学];
N [自然科学总论];
学科分类号
:
07 ;
0710 ;
09 ;
摘要
:
引用
收藏
页码:69 / 70
页数:2
相关论文
共 23 条
[21]
SHOHET SB, 1977, LIPID METABOLISM MAM, V1, P191
[22]
BIOCHEMICAL-STUDIES IN THE LIVER AND MUSCLE OF PATIENTS WITH ZELLWEGER SYNDROME
TRIJBELS, JMF
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
TRIJBELS, JMF
BERDEN, JA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
BERDEN, JA
MONNENS, LAH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
MONNENS, LAH
WILLEMS, JL
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
WILLEMS, JL
JANSSEN, AJM
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
JANSSEN, AJM
SCHUTGENS, RBH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
SCHUTGENS, RBH
VANDENBROEKVANESSEN, M
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
VANDENBROEKVANESSEN, M
[J].
PEDIATRIC RESEARCH,
1983,
17
(06)
: 514
-
517
[23]
METABOLIC DISORDER SIMILAR TO ZELLWEGER SYNDROME WITH HEPATIC ACATALASIA AND ABSENCE OF PEROXISOMES, ALTERED CONTENT AND REDOX STATE OF CYTOCHROMES, AND INFANTILE CIRRHOSIS WITH HEMOSIDEROSIS
VERSMOLD, HT
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
VERSMOLD, HT
BREMER, HI
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
BREMER, HI
HERZOG, V
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
HERZOG, V
SIEGEL, G
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
SIEGEL, G
BASSEWITZ, DBV
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
BASSEWITZ, DBV
IRLE, U
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
IRLE, U
VOSS, HV
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
VOSS, HV
LOMBECK, I
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
LOMBECK, I
BRAUSER, B
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
BRAUSER, B
[J].
EUROPEAN JOURNAL OF PEDIATRICS,
1977,
124
(04)
: 261
-
275
←
1
2
3
→
共 23 条
[21]
SHOHET SB, 1977, LIPID METABOLISM MAM, V1, P191
[22]
BIOCHEMICAL-STUDIES IN THE LIVER AND MUSCLE OF PATIENTS WITH ZELLWEGER SYNDROME
TRIJBELS, JMF
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
TRIJBELS, JMF
BERDEN, JA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
BERDEN, JA
MONNENS, LAH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
MONNENS, LAH
WILLEMS, JL
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
WILLEMS, JL
JANSSEN, AJM
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
JANSSEN, AJM
SCHUTGENS, RBH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
SCHUTGENS, RBH
VANDENBROEKVANESSEN, M
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV AMSTERDAM,DEPT BIOCHEM,AMSTERDAM,NETHERLANDS
VANDENBROEKVANESSEN, M
[J].
PEDIATRIC RESEARCH,
1983,
17
(06)
: 514
-
517
[23]
METABOLIC DISORDER SIMILAR TO ZELLWEGER SYNDROME WITH HEPATIC ACATALASIA AND ABSENCE OF PEROXISOMES, ALTERED CONTENT AND REDOX STATE OF CYTOCHROMES, AND INFANTILE CIRRHOSIS WITH HEMOSIDEROSIS
VERSMOLD, HT
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
VERSMOLD, HT
BREMER, HI
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
BREMER, HI
HERZOG, V
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
HERZOG, V
SIEGEL, G
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
SIEGEL, G
BASSEWITZ, DBV
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
BASSEWITZ, DBV
IRLE, U
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
IRLE, U
VOSS, HV
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
VOSS, HV
LOMBECK, I
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
LOMBECK, I
BRAUSER, B
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNICH,CHILDRENS HOSP,DIV NEONATOL,D-8000 MUNICH 2,FED REP GER
BRAUSER, B
[J].
EUROPEAN JOURNAL OF PEDIATRICS,
1977,
124
(04)
: 261
-
275
←
1
2
3
→