PANTETHINE AND CYSTAMINE DEPLETE CYSTINE FROM CYSTINOTIC FIBROBLASTS VIA EFFLUX OF CYSTEAMINE-CYSTEINE MIXED DISULFIDE

被引:40
作者
BUTLER, JD [1 ]
ZATZ, M [1 ]
机构
[1] NIMH,CELL BIOL LAB,BIOCHEM PHARMACOL UNIT,BETHESDA,MD 20205
关键词
D O I
10.1172/JCI111436
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:411 / 416
页数:6
相关论文
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