A COMPARISON OF THE EFFECTIVENESS OF CYSTEAMINE AND PHOSPHOCYSTEAMINE IN ELEVATING PLASMA CYSTEAMINE CONCENTRATION AND DECREASING LEUKOCYTE FREE CYSTINE IN NEPHROPATHIC CYSTINOSIS

被引：49

作者：

SMOLIN, LA

CLARK, KF

THOENE, JG

GAHL, WA

SCHNEIDER, JA

机构：

[1] UNIV CALIF SAN DIEGO, SCH MED, DEPT PEDIAT, M-009-F, LA JOLLA, CA 92093 USA

[2] NICHHD, HUMAN GENET BRANCH, HUMAN BIOCHEM GENET SECT, BETHESDA, MD 20892 USA

[3] UNIV MICHIGAN, SCH PUBL HLTH, DEPT PEDIAT, ANN ARBOR, MI 48109 USA

来源：

PEDIATRIC RESEARCH | 1988年 / 23卷 / 06期

关键词：

D O I：

10.1203/00006450-198806000-00018

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

引用

页码：616 / 620

页数：5

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