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HUMAN-LIVER SULFAMATE SULFOHYDROLASE - DETERMINATIONS OF NATIVE PROTEIN AND SUBUNIT MR VALUES AND INFLUENCE OF SUBSTRATE AGYLCONE STRUCTURE ON CATALYTIC PROPERTIES
被引:50
作者
:
FREEMAN, C
论文数:
0
引用数:
0
h-index:
0
FREEMAN, C
HOPWOOD, JJ
论文数:
0
引用数:
0
h-index:
0
HOPWOOD, JJ
机构
:
来源
:
BIOCHEMICAL JOURNAL
|
1986年
/ 234卷
/ 01期
关键词
:
D O I
:
10.1042/bj2340083
中图分类号
:
Q5 [生物化学];
Q7 [分子生物学];
学科分类号
:
071010 ;
081704 ;
摘要
:
引用
收藏
页码:83 / 92
页数:10
相关论文
共 28 条
[11]
RADIOLABELED OLIGOSACCHARIDES AS SUBSTRATES FOR THE ESTIMATION OF SULFAMIDASE AND THE DETECTION OF THE SANFILIPPO TYPE-A SYNDROME
HOPWOOD, JJ
论文数:
0
引用数:
0
h-index:
0
HOPWOOD, JJ
ELLIOTT, H
论文数:
0
引用数:
0
h-index:
0
ELLIOTT, H
[J].
CLINICA CHIMICA ACTA,
1981,
112
(01)
: 55
-
66
[12]
SULFAMIDASE ACTIVITY IN LEUKOCYTES, CULTURED SKIN FIBROBLASTS AND AMNIOTIC CELLS - DIAGNOSIS OF THE SANFILIPPO-A-SYNDROME WITH THE USE OF A RADIOLABELED DISACCHARIDE SUBSTRATE
HOPWOOD, JJ
论文数:
0
引用数:
0
h-index:
0
HOPWOOD, JJ
ELLIOTT, H
论文数:
0
引用数:
0
h-index:
0
ELLIOTT, H
[J].
CLINICAL SCIENCE,
1981,
61
(06)
: 729
-
735
[13]
ALPHA-L-IDURONIDASE, BETA-D-GLUCURONIDASE, AND 2-SULFO-L-IDURONATE 2-SULFATASE - PREPARATION AND CHARACTERIZATION OF RADIOACTIVE SUBSTRATES FROM HEPARIN
HOPWOOD, JJ
论文数:
0
引用数:
0
h-index:
0
机构:
Department of Chemical Pathology, The Adelaide Children's Hospital, Inc., North Adelaide
HOPWOOD, JJ
[J].
CARBOHYDRATE RESEARCH,
1979,
69
(MAR)
: 203
-
216
[14]
JACOBSSON I, 1984, J BIOL CHEM, V259, P1056
[15]
JACOBSSON I, 1980, J BIOL CHEM, V255, P5094
[16]
MUCOPOLYSACCHARIDOSIS III A (SANFILIPPO A DISEASE) - DEFICIENCY OF A HEPARIN SULFAMIDASE IN SKIN FIBROBLASTS AND LEUKOCYTES
KRESSE, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNSTER,INST PHYSIOL CHEM,MUNSTER,WEST GERMANY
UNIV MUNSTER,INST PHYSIOL CHEM,MUNSTER,WEST GERMANY
KRESSE, H
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1973,
54
(03)
: 1111
-
1118
[17]
A HIGH RECOVERY METHOD FOR CONCENTRATING MICROGRAM QUANTITIES OF PROTEIN FROM LARGE VOLUMES OF SOLUTION
MAHURAN, D
论文数:
0
引用数:
0
h-index:
0
机构:
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
MAHURAN, D
CLEMENTS, P
论文数:
0
引用数:
0
h-index:
0
机构:
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
CLEMENTS, P
CARRELLA, M
论文数:
0
引用数:
0
h-index:
0
机构:
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
CARRELLA, M
STRASBERG, PM
论文数:
0
引用数:
0
h-index:
0
机构:
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
STRASBERG, PM
[J].
ANALYTICAL BIOCHEMISTRY,
1983,
129
(02)
: 513
-
516
[18]
A RAPID 4 COLUMN PURIFICATION OF 2-DEOXY-D-GLUCOSIDE-2-SULPHAMATE SULFOHYDROLASE FROM HUMAN-LIVER
MAHURAN, D
论文数:
0
引用数:
0
h-index:
0
机构:
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
MAHURAN, D
CLEMENTS, P
论文数:
0
引用数:
0
h-index:
0
机构:
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
CLEMENTS, P
HOPWOOD, J
论文数:
0
引用数:
0
h-index:
0
机构:
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
HOPWOOD, J
[J].
BIOCHIMICA ET BIOPHYSICA ACTA,
1983,
757
(03)
: 359
-
365
[19]
MARKWELL MK, 1978, ANAL BIOCHEM, V87, P211
[20]
SANFILIPPO A SYNDROME - SULFAMIDASE DEFICIENCY IN CULTURED SKIN FIBROBLASTS AND LIVER
MATALON, R
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CHICAGO,PRITZKER SCH MED,DEPT PEDIAT,CHICAGO,IL 60637
MATALON, R
DORFMAN, A
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CHICAGO,PRITZKER SCH MED,DEPT PEDIAT,CHICAGO,IL 60637
DORFMAN, A
[J].
JOURNAL OF CLINICAL INVESTIGATION,
1974,
54
(04)
: 907
-
912
←
1
2
3
→
共 28 条
[11]
RADIOLABELED OLIGOSACCHARIDES AS SUBSTRATES FOR THE ESTIMATION OF SULFAMIDASE AND THE DETECTION OF THE SANFILIPPO TYPE-A SYNDROME
HOPWOOD, JJ
论文数:
0
引用数:
0
h-index:
0
HOPWOOD, JJ
ELLIOTT, H
论文数:
0
引用数:
0
h-index:
0
ELLIOTT, H
[J].
CLINICA CHIMICA ACTA,
1981,
112
(01)
: 55
-
66
[12]
SULFAMIDASE ACTIVITY IN LEUKOCYTES, CULTURED SKIN FIBROBLASTS AND AMNIOTIC CELLS - DIAGNOSIS OF THE SANFILIPPO-A-SYNDROME WITH THE USE OF A RADIOLABELED DISACCHARIDE SUBSTRATE
HOPWOOD, JJ
论文数:
0
引用数:
0
h-index:
0
HOPWOOD, JJ
ELLIOTT, H
论文数:
0
引用数:
0
h-index:
0
ELLIOTT, H
[J].
CLINICAL SCIENCE,
1981,
61
(06)
: 729
-
735
[13]
ALPHA-L-IDURONIDASE, BETA-D-GLUCURONIDASE, AND 2-SULFO-L-IDURONATE 2-SULFATASE - PREPARATION AND CHARACTERIZATION OF RADIOACTIVE SUBSTRATES FROM HEPARIN
HOPWOOD, JJ
论文数:
0
引用数:
0
h-index:
0
机构:
Department of Chemical Pathology, The Adelaide Children's Hospital, Inc., North Adelaide
HOPWOOD, JJ
[J].
CARBOHYDRATE RESEARCH,
1979,
69
(MAR)
: 203
-
216
[14]
JACOBSSON I, 1984, J BIOL CHEM, V259, P1056
[15]
JACOBSSON I, 1980, J BIOL CHEM, V255, P5094
[16]
MUCOPOLYSACCHARIDOSIS III A (SANFILIPPO A DISEASE) - DEFICIENCY OF A HEPARIN SULFAMIDASE IN SKIN FIBROBLASTS AND LEUKOCYTES
KRESSE, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MUNSTER,INST PHYSIOL CHEM,MUNSTER,WEST GERMANY
UNIV MUNSTER,INST PHYSIOL CHEM,MUNSTER,WEST GERMANY
KRESSE, H
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1973,
54
(03)
: 1111
-
1118
[17]
A HIGH RECOVERY METHOD FOR CONCENTRATING MICROGRAM QUANTITIES OF PROTEIN FROM LARGE VOLUMES OF SOLUTION
MAHURAN, D
论文数:
0
引用数:
0
h-index:
0
机构:
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
MAHURAN, D
CLEMENTS, P
论文数:
0
引用数:
0
h-index:
0
机构:
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
CLEMENTS, P
CARRELLA, M
论文数:
0
引用数:
0
h-index:
0
机构:
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
CARRELLA, M
STRASBERG, PM
论文数:
0
引用数:
0
h-index:
0
机构:
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
STRASBERG, PM
[J].
ANALYTICAL BIOCHEMISTRY,
1983,
129
(02)
: 513
-
516
[18]
A RAPID 4 COLUMN PURIFICATION OF 2-DEOXY-D-GLUCOSIDE-2-SULPHAMATE SULFOHYDROLASE FROM HUMAN-LIVER
MAHURAN, D
论文数:
0
引用数:
0
h-index:
0
机构:
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
MAHURAN, D
CLEMENTS, P
论文数:
0
引用数:
0
h-index:
0
机构:
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
CLEMENTS, P
HOPWOOD, J
论文数:
0
引用数:
0
h-index:
0
机构:
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
ADELAIDE CHILDRENS HOSP,DEPT CHEM PATHOL,N ADELAIDE,SA 5006,AUSTRALIA
HOPWOOD, J
[J].
BIOCHIMICA ET BIOPHYSICA ACTA,
1983,
757
(03)
: 359
-
365
[19]
MARKWELL MK, 1978, ANAL BIOCHEM, V87, P211
[20]
SANFILIPPO A SYNDROME - SULFAMIDASE DEFICIENCY IN CULTURED SKIN FIBROBLASTS AND LIVER
MATALON, R
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CHICAGO,PRITZKER SCH MED,DEPT PEDIAT,CHICAGO,IL 60637
MATALON, R
DORFMAN, A
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CHICAGO,PRITZKER SCH MED,DEPT PEDIAT,CHICAGO,IL 60637
DORFMAN, A
[J].
JOURNAL OF CLINICAL INVESTIGATION,
1974,
54
(04)
: 907
-
912
←
1
2
3
→