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HUMAN BETA-GLUCURONIDASE .2. FATE OF INFUSED HUMAN PLACENTAL BETA-GLUCURONIDASE IN RAT
被引:52
作者
:
ACHORD, D
论文数:
0
引用数:
0
h-index:
0
机构:
ST LOUIS CHILDRENS HOSP, DIV MED GENET, ST LOUIS, MO 63110 USA
ACHORD, D
BROT, F
论文数:
0
引用数:
0
h-index:
0
机构:
ST LOUIS CHILDRENS HOSP, DIV MED GENET, ST LOUIS, MO 63110 USA
BROT, F
GONZALEZNORIEGA, A
论文数:
0
引用数:
0
h-index:
0
机构:
ST LOUIS CHILDRENS HOSP, DIV MED GENET, ST LOUIS, MO 63110 USA
GONZALEZNORIEGA, A
SLY, W
论文数:
0
引用数:
0
h-index:
0
机构:
ST LOUIS CHILDRENS HOSP, DIV MED GENET, ST LOUIS, MO 63110 USA
SLY, W
STAHL, P
论文数:
0
引用数:
0
h-index:
0
机构:
ST LOUIS CHILDRENS HOSP, DIV MED GENET, ST LOUIS, MO 63110 USA
STAHL, P
机构
:
[1]
ST LOUIS CHILDRENS HOSP, DIV MED GENET, ST LOUIS, MO 63110 USA
[2]
WASHINGTON UNIV, SCH MED, EDWARD MALLINCKRODT DEPT PEDIAT, ST LOUIS, MO 63110 USA
[3]
WASHINGTON UNIV, SCH MED, DEPT PHYSIOL & BIOPHYS, ST LOUIS, MO 63110 USA
来源
:
PEDIATRIC RESEARCH
|
1977年
/ 11卷
/ 07期
关键词
:
D O I
:
10.1203/00006450-197707000-00008
中图分类号
:
R72 [儿科学];
学科分类号
:
100202 ;
摘要
:
引用
收藏
页码:816 / 822
页数:7
相关论文
共 30 条
[1]
ACHORD DT, 1975, AM J HUM GENET, V27, pA10
[2]
BRADY RO, 1975, FED PROC, V34, P1310
[3]
REPLACEMENT THERAPY FOR INHERITED ENZYME DEFICIENCY - USE OF PURIFIED GLUCOCEREBROSIDASE IN GAUCHERS-DISEASE
BRADY, RO
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV & METAB NEUROL BRANCH,BLDG 10,RM 3003,BETHESDA,MD 20014
NINDS,DEV & METAB NEUROL BRANCH,BLDG 10,RM 3003,BETHESDA,MD 20014
BRADY, RO
PENTCHEV, PG
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV & METAB NEUROL BRANCH,BLDG 10,RM 3003,BETHESDA,MD 20014
NINDS,DEV & METAB NEUROL BRANCH,BLDG 10,RM 3003,BETHESDA,MD 20014
PENTCHEV, PG
GAL, AE
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV & METAB NEUROL BRANCH,BLDG 10,RM 3003,BETHESDA,MD 20014
NINDS,DEV & METAB NEUROL BRANCH,BLDG 10,RM 3003,BETHESDA,MD 20014
GAL, AE
HIBBERT, SR
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV & METAB NEUROL BRANCH,BLDG 10,RM 3003,BETHESDA,MD 20014
NINDS,DEV & METAB NEUROL BRANCH,BLDG 10,RM 3003,BETHESDA,MD 20014
HIBBERT, SR
DEKABAN, AS
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV & METAB NEUROL BRANCH,BLDG 10,RM 3003,BETHESDA,MD 20014
NINDS,DEV & METAB NEUROL BRANCH,BLDG 10,RM 3003,BETHESDA,MD 20014
DEKABAN, AS
[J].
NEW ENGLAND JOURNAL OF MEDICINE,
1974,
291
(19)
: 989
-
993
[4]
REPLACEMENT THERAPY FOR INHERITED ENZYME DEFICIENCY - USE OF PURIFIED CERAMIDETRIHEXOSIDASE IN FABRYS-DISEASE
BRADY, RO
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
BRADY, RO
TALLMAN, JF
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
TALLMAN, JF
JOHNSON, WG
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
JOHNSON, WG
GAL, AE
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
GAL, AE
LEAHY, WR
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
LEAHY, WR
QUIRK, JM
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
QUIRK, JM
DEKABAN, AS
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
DEKABAN, AS
[J].
NEW ENGLAND JOURNAL OF MEDICINE,
1973,
289
(01)
: 9
-
14
[5]
IN-VITRO CORRECTION OF DEFICIENT HUMAN FIBROBLASTS BY BETA-GLUCURONIDASE FROM DIFFERENT HUMAN SOURCES
BROT, FE
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
BROT, FE
GLASER, JH
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
GLASER, JH
ROOZEN, KJ
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
ROOZEN, KJ
SLY, WS
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
SLY, WS
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1974,
57
(01)
: 1
-
8
[6]
de Barsy T, 1973, Birth Defects Orig Artic Ser, V9, P184
[7]
TOWARD ENZYME THERAPY FOR LYSOSOMAL STORAGE DISEASES
DESNICK, RJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MINNESOTA, DEPT PEDIAT, MINNEAPOLIS, MN 55455 USA
DESNICK, RJ
THORPE, SR
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MINNESOTA, DEPT PEDIAT, MINNEAPOLIS, MN 55455 USA
THORPE, SR
FIDDLER, MB
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MINNESOTA, DEPT PEDIAT, MINNEAPOLIS, MN 55455 USA
FIDDLER, MB
[J].
PHYSIOLOGICAL REVIEWS,
1976,
56
(01)
: 57
-
99
[8]
TISSUE FRACTIONATION STUDIES .6. INTRACELLULAR DISTRIBUTION PATTERNS OF ENZYMES IN RAT-LIVER TISSUE
DUVE, CD
论文数:
0
引用数:
0
h-index:
0
DUVE, CD
PRESSMAN, BC
论文数:
0
引用数:
0
h-index:
0
PRESSMAN, BC
GIANETTO, R
论文数:
0
引用数:
0
h-index:
0
GIANETTO, R
WATTIAUX, R
论文数:
0
引用数:
0
h-index:
0
WATTIAUX, R
APPELMANS, F
论文数:
0
引用数:
0
h-index:
0
APPELMANS, F
[J].
BIOCHEMICAL JOURNAL,
1955,
60
(1-4)
: 604
-
617
[9]
HUMAN BETA-GLUCURONIDASE .1. RECOGNITION AND UPTAKE BY ANIMAL FIBROBLASTS SUGGESTS ANIMAL-MODELS FOR ENZYME REPLACEMENT STUDIES
FRANKEL, HA
论文数:
0
引用数:
0
h-index:
0
机构:
ST LOUIS CHILDRENS HOSP,DEPT PEDIAT,DIV MED GENET,ST LOUIS,MO 63110
FRANKEL, HA
GLASER, JH
论文数:
0
引用数:
0
h-index:
0
机构:
ST LOUIS CHILDRENS HOSP,DEPT PEDIAT,DIV MED GENET,ST LOUIS,MO 63110
GLASER, JH
SLY, WS
论文数:
0
引用数:
0
h-index:
0
机构:
ST LOUIS CHILDRENS HOSP,DEPT PEDIAT,DIV MED GENET,ST LOUIS,MO 63110
SLY, WS
[J].
PEDIATRIC RESEARCH,
1977,
11
(07)
: 811
-
816
[10]
GLASER JH, 1973, J LAB CLIN MED, V82, P969
←
1
2
3
→
共 30 条
[1]
ACHORD DT, 1975, AM J HUM GENET, V27, pA10
[2]
BRADY RO, 1975, FED PROC, V34, P1310
[3]
REPLACEMENT THERAPY FOR INHERITED ENZYME DEFICIENCY - USE OF PURIFIED GLUCOCEREBROSIDASE IN GAUCHERS-DISEASE
BRADY, RO
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV & METAB NEUROL BRANCH,BLDG 10,RM 3003,BETHESDA,MD 20014
NINDS,DEV & METAB NEUROL BRANCH,BLDG 10,RM 3003,BETHESDA,MD 20014
BRADY, RO
PENTCHEV, PG
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV & METAB NEUROL BRANCH,BLDG 10,RM 3003,BETHESDA,MD 20014
NINDS,DEV & METAB NEUROL BRANCH,BLDG 10,RM 3003,BETHESDA,MD 20014
PENTCHEV, PG
GAL, AE
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV & METAB NEUROL BRANCH,BLDG 10,RM 3003,BETHESDA,MD 20014
NINDS,DEV & METAB NEUROL BRANCH,BLDG 10,RM 3003,BETHESDA,MD 20014
GAL, AE
HIBBERT, SR
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV & METAB NEUROL BRANCH,BLDG 10,RM 3003,BETHESDA,MD 20014
NINDS,DEV & METAB NEUROL BRANCH,BLDG 10,RM 3003,BETHESDA,MD 20014
HIBBERT, SR
DEKABAN, AS
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV & METAB NEUROL BRANCH,BLDG 10,RM 3003,BETHESDA,MD 20014
NINDS,DEV & METAB NEUROL BRANCH,BLDG 10,RM 3003,BETHESDA,MD 20014
DEKABAN, AS
[J].
NEW ENGLAND JOURNAL OF MEDICINE,
1974,
291
(19)
: 989
-
993
[4]
REPLACEMENT THERAPY FOR INHERITED ENZYME DEFICIENCY - USE OF PURIFIED CERAMIDETRIHEXOSIDASE IN FABRYS-DISEASE
BRADY, RO
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
BRADY, RO
TALLMAN, JF
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
TALLMAN, JF
JOHNSON, WG
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
JOHNSON, WG
GAL, AE
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
GAL, AE
LEAHY, WR
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
LEAHY, WR
QUIRK, JM
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
QUIRK, JM
DEKABAN, AS
论文数:
0
引用数:
0
h-index:
0
机构:
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
NINDS,DEV METAB NEUROL BRANCH,BETHESDA,MD 20014
DEKABAN, AS
[J].
NEW ENGLAND JOURNAL OF MEDICINE,
1973,
289
(01)
: 9
-
14
[5]
IN-VITRO CORRECTION OF DEFICIENT HUMAN FIBROBLASTS BY BETA-GLUCURONIDASE FROM DIFFERENT HUMAN SOURCES
BROT, FE
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
BROT, FE
GLASER, JH
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
GLASER, JH
ROOZEN, KJ
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
ROOZEN, KJ
SLY, WS
论文数:
0
引用数:
0
h-index:
0
机构:
WASHINGTON UNIV, SCH MED, DEPT PEDIAT, ST LOUIS, MO 63110 USA
SLY, WS
[J].
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS,
1974,
57
(01)
: 1
-
8
[6]
de Barsy T, 1973, Birth Defects Orig Artic Ser, V9, P184
[7]
TOWARD ENZYME THERAPY FOR LYSOSOMAL STORAGE DISEASES
DESNICK, RJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MINNESOTA, DEPT PEDIAT, MINNEAPOLIS, MN 55455 USA
DESNICK, RJ
THORPE, SR
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MINNESOTA, DEPT PEDIAT, MINNEAPOLIS, MN 55455 USA
THORPE, SR
FIDDLER, MB
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV MINNESOTA, DEPT PEDIAT, MINNEAPOLIS, MN 55455 USA
FIDDLER, MB
[J].
PHYSIOLOGICAL REVIEWS,
1976,
56
(01)
: 57
-
99
[8]
TISSUE FRACTIONATION STUDIES .6. INTRACELLULAR DISTRIBUTION PATTERNS OF ENZYMES IN RAT-LIVER TISSUE
DUVE, CD
论文数:
0
引用数:
0
h-index:
0
DUVE, CD
PRESSMAN, BC
论文数:
0
引用数:
0
h-index:
0
PRESSMAN, BC
GIANETTO, R
论文数:
0
引用数:
0
h-index:
0
GIANETTO, R
WATTIAUX, R
论文数:
0
引用数:
0
h-index:
0
WATTIAUX, R
APPELMANS, F
论文数:
0
引用数:
0
h-index:
0
APPELMANS, F
[J].
BIOCHEMICAL JOURNAL,
1955,
60
(1-4)
: 604
-
617
[9]
HUMAN BETA-GLUCURONIDASE .1. RECOGNITION AND UPTAKE BY ANIMAL FIBROBLASTS SUGGESTS ANIMAL-MODELS FOR ENZYME REPLACEMENT STUDIES
FRANKEL, HA
论文数:
0
引用数:
0
h-index:
0
机构:
ST LOUIS CHILDRENS HOSP,DEPT PEDIAT,DIV MED GENET,ST LOUIS,MO 63110
FRANKEL, HA
GLASER, JH
论文数:
0
引用数:
0
h-index:
0
机构:
ST LOUIS CHILDRENS HOSP,DEPT PEDIAT,DIV MED GENET,ST LOUIS,MO 63110
GLASER, JH
SLY, WS
论文数:
0
引用数:
0
h-index:
0
机构:
ST LOUIS CHILDRENS HOSP,DEPT PEDIAT,DIV MED GENET,ST LOUIS,MO 63110
SLY, WS
[J].
PEDIATRIC RESEARCH,
1977,
11
(07)
: 811
-
816
[10]
GLASER JH, 1973, J LAB CLIN MED, V82, P969
←
1
2
3
→