IMPROVEMENT OF CLINICAL AND MRI FINDINGS IN A BOY WITH ADRENOLEUKODYSTROPHY BY DIETARY ERUCIC-ACID THERAPY

被引：5

作者：

MAEDA, K

SUZUKI, Y

YAJIMA, S

ASANO, J

YAMAGUCHI, S

MATSUMOTO, N

BOREL, J

MOSER, HW

ORII, T

机构：

[1] GIFU UNIV,SCH MED,DEPT PEDIAT,TSUKASA MACHI 40,GIFU 500,JAPAN

[2] SHIZUOKA SAISEIKAI GEN HOSP,DEPT PEDIAT,SHIZUOKA,JAPAN

[3] JOHNS HOPKINS UNIV,KENNEDY KRIEGER INST,BALTIMORE,MD 21218

来源：

BRAIN & DEVELOPMENT | 1992年 / 14卷 / 06期

关键词：

ADRENOLEUKODYSTROPHY; ERUCIC ACID THERAPY; MAGNETIC RESONANCE IMAGING;

D O I：

10.1016/S0387-7604(12)80350-0

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

A 5-year-old boy with adrenoleukodystrophy, with clinical symptoms of visual, mental and motor disturbances which progressed rapidly, was treated with Lorenzo's oil consisting 1 volume of glyceryl trierucate and 4 volumes of glyceryl trioleate. Five months after initiation of this therapy, ability to swallow was enhanced and T2-weighted magnetic resonance imaging of the brain revealed regression of high intensity area of the parieto-occipital white matter.

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页码：409 / 412

页数：4

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